Double-chambered left ventricle in a patient with Wolff–Parkinson–White syndrome: A case report

Congenital heart diseases like non-compaction cardiomyopathy, congenital left ventricular diverticulum, and aneurysm are potential triggers of arrhythmias. Any condition affecting the correct embryological development of the atrioventricular annuli might potentially be the basis for accessory pathways and WPW Syndrome; we are describing a first reported association with a rare congenital heart disease, a double-chambered left ventricle. Although typically diagnosed in pediatric age, it can remain asymptomatic and incidentally found in adulthood. The embryological alteration in the myocardial compaction might explain both the formation of an accessory chamber and the persistence of an anomalous electrical connection between atria and ventricles.