一名表现为急性阑尾炎的儿童腹腔内横纹肌肉瘤。

IF 1.1 4区 医学 Q3 SURGERY
M C Moolamannil, H Khan, S Karim
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引用次数: 0

摘要

横纹肌肉瘤(RMS)是一种软组织肉瘤,可发生于人体几乎任何部位的肌肉或纤维组织。横纹肌肉瘤的两个主要亚型是肺泡型和胚胎型,而两个较罕见的亚型是多形性(通常发生在成人身上)和纺锤形细胞/硬化变异型(通常发生在儿童身上)。红斑狼疮通常累及四肢、头颈部或泌尿生殖系统。虽然它可以发生在身体的任何部位,但其他受累部位很少见,而且由于对周围组织和器官的大量影响,通常只在晚期才出现。我们介绍了一例罕见病例,患儿出现急腹症的症状和体征,但术中发现其腹壁前部有一个出血坏死性肿块。经组织学证实,这是一个胚胎型红斑狼疮。
本文章由计算机程序翻译,如有差异,请以英文原文为准。
Intra-abdominal rhabdomyosarcoma in a paediatric patient presenting as acute appendicitis.

Rhabdomyosarcoma (RMS) is a form of soft tissue sarcoma that can arise from muscle or fibrous tissue almost anywhere in the body. The two major subtypes of RMS are alveolar and embryonal, whereas the two rarer subtypes are pleomorphic, which typically occurs in adults, and the spindle cell/sclerosing variant, typically seen in children. RMS usually involves the extremities, the head and neck or the genitourinary system. Although it can arise from anywhere in the body, other sites of involvement are rare and usually present only at an advanced stage owing to a mass effect on surrounding tissues and organs. We present a rare case of a child who presented with the signs and symptoms of an acute abdomen, but intraoperatively was found to have a bleeding necrotic mass arising from the anterior abdominal wall. This was histologically confirmed to be a RMS of the embryonal type.

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来源期刊
CiteScore
2.40
自引率
0.00%
发文量
316
期刊介绍: The Annals of The Royal College of Surgeons of England is the official scholarly research journal of the Royal College of Surgeons and is published eight times a year in January, February, March, April, May, July, September and November. The main aim of the journal is to publish high-quality, peer-reviewed papers that relate to all branches of surgery. The Annals also includes letters and comments, a regular technical section, controversial topics, CORESS feedback and book reviews. The editorial board is composed of experts from all the surgical specialties.
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