表现为软腭水肿和悬雍垂坏死的胚胎横纹肌肉瘤:病例报告和文献综述

O. C. Wengerman, Jonathan Maya Epelstein, Hector De La Garza Hesles, María J. Sanabrais López, Michelle Mizrahi Yaffe
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引用次数: 0

摘要

横纹肌肉瘤(RMS)是一种影响骨骼肌的恶性肿瘤,通常发生在儿童的头颈部。据报道,有少数病例的横纹肌肉瘤发生在口腔。该病患者的预后取决于许多临床和生物学因素,包括年龄、肿瘤位置、组织病理学亚型以及确诊时肿瘤是否已经扩散。本病例报告和文献综述主要介绍了葡萄膜胚胎性红斑狼疮的一种不寻常表现。报告描述了一例年幼的墨西哥儿童,患者出现水肿、软腭肿胀和悬雍垂坏死等症状。作者讨论了这种肿瘤的特征、管理和治疗,对这种罕见病症的预后和治疗方法提供了有价值的见解,并考虑到由于患者年龄较小,头颈部的解剖结构非常重要,因此头颈部可能是一个具有挑战性的治疗部位。
本文章由计算机程序翻译,如有差异,请以英文原文为准。
Embryonal rhabdomyosarcoma presenting as edema of the soft palate and necrosis of the uvula: a case report and review of the literature
Rhabdomyosarcoma (RMS) is a malignant tumor that affects skeletal muscles, typically found in the head and neck region of children. There have been a few reported cases of RMS occurring in the oral cavity. The prognosis of a patient with this condition depends on many clinical and biological factors, including age, the location of the tumor, histopathological subtype, and whether it has spread at the time of diagnosis. This case report and literature review focus on an unusual presentation of embryonal RMS in the uvula. The report described a case of a young Mexican child presented with symptoms such as edema, swelling of the soft palate, and necrosis of the uvula. The authors discuss the characteristics, management, and treatment of this neoplasm, providing valuable insights on the prognosis and therapeutic approaches for this rare condition and considering that the head and neck region can be a challenging site to treat due to the young age of the patient and the critical anatomy of this area.
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