Giuseppe Paviglianiti, Roberta Cristina Avallone, Valentina Cariello, Marzia Vaccaro, Floriana Di Marco, Rocco Minelli, Francesca Antonia De Chiara, Francesco Esposito, Dolores Ferrara, Antonio Rossi, Paolo Pizzicato, Eugenio Rossi
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引用次数: 0
摘要
胆道闭锁(BA)是一种先天性疾病,当肝脏外胆管缺失或不足时,会导致肝纤维化、门静脉高压,并最终导致肝硬化。这是新生儿持续阻塞性黄疸最常见的原因,持续时间超过两周。腹部超声(US)是诊断 BA 的主要成像技术,而计算机断层扫描(CT)则用于更复杂的病例。诊断 BA 的金标准仍然是术中胆管造影和肝活检。BA的治疗通常包括葛西肝门肠造瘘术,但由于诊断延误和疾病晚期,一些患者仍需要进行肝移植。在本研究中,作者介绍了一名 3 个月大胆道闭锁婴儿的病例及其超声特征,该婴儿因疾病晚期而接受了肝移植。鉴于及时手术干预的重要意义,影像学检查的主要目的是提供及时诊断。
Biliary atresia in a 3-month-old infant (case report).
Biliary atresia (BA) is a congenital disease that occurs when extrahepatic bile ducts are either absent or deficient, resulting in liver fibrosis, portal hypertension, and eventually cirrhosis. It is the most common cause of persistent obstructive jaundice in newborns lasting more than two weeks is this condition. Abdominal ultrasound (US) is the primary imaging technique used to diagnose BA, while computed tomography (CT) is reserved for more complex cases. The gold standard for diagnosing BA is still intraoperative cholangiogram with liver biopsy. Treatment for BA usually involves Kasai hepatoportoenterostomy, but some patients still require liver transplantation due to diagnostic delays and advanced disease. In this study, the authors present the case of a 3-month-old infant with biliary atresia and its ultrasound characteristics, who underwent liver transplantation due to advanced disease. The primary objective of imaging is to provide a prompt diagnosis, given the crucial significance of timely surgical intervention.
期刊介绍:
The Journal of Ultrasound is the official journal of the Italian Society for Ultrasound in Medicine and Biology (SIUMB). The journal publishes original contributions (research and review articles, case reports, technical reports and letters to the editor) on significant advances in clinical diagnostic, interventional and therapeutic applications, clinical techniques, the physics, engineering and technology of ultrasound in medicine and biology, and in cross-sectional diagnostic imaging. The official language of Journal of Ultrasound is English.