气道受累的副肿瘤性天疱疮

IF 0.8 Q4 RESPIRATORY SYSTEM
Oscar A. Estrada Paz, Timothy J. Young
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引用次数: 0

摘要

我们报告了一例副肿瘤性丘疹性荨麻疹患者,该患者因支气管炎闭塞而出现急性低氧血症性呼吸衰竭,在接受大剂量全身皮质类固醇、利妥昔单抗、烟酰胺和强力霉素治疗后病情有所好转。据我们所知,这是第一份关于副肿瘤性丘疹性荨麻疹累及气道的报告,其中包括烟酰胺和强力霉素作为治疗手段,并显示出治疗反应。
本文章由计算机程序翻译,如有差异,请以英文原文为准。
Paraneoplastic pemphigus with airway involvement

We report a case of paraneoplastic pemphigus presenting with acute hypoxemic respiratory failure due to bronchiolitis obliterans which improved with high dose systemic corticosteroids, rituximab, niacinamide and doxycycline. This is the first report, to our knowledge, of paraneoplastic pemphigus with airway involvement which included niacinamide and doxycycline as therapy and demonstrated treatment response.

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来源期刊
Respiratory Medicine Case Reports
Respiratory Medicine Case Reports RESPIRATORY SYSTEM-
CiteScore
2.10
自引率
0.00%
发文量
213
审稿时长
87 days
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