幼年路易体痴呆症表现为冷漠和无情感。

IF 0.6 4区医学 Q4 CLINICAL NEUROLOGY

Neurocase Pub Date : 2023-12-01 Epub Date: 2024-05-16 DOI:10.1080/13554794.2024.2354545

Stefania Kaninia, Rosaleen A McCarthy, Zia Saad, George P Pengas

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引用次数: 0

摘要

幼年痴呆症的诊断会给临床医生带来巨大的挑战。我们为您介绍一位表现非常不寻常的路易体痴呆症年轻患者。他缺乏运动症状，而且明显冷漠，因此延误了诊断。他的症状被认为是抑郁症所致，因为他的结构成像正常，而且他的表现具有精神病学性质。对他进行了广泛的检查。HMPAO-SPECT 提供了结构性神经退行性过程的证据。心脏 MIBG 确诊。

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Young-onset dementia with Lewy Bodies presenting with apathy and alexithymia.

A diagnosis of young-onset dementia can pose a significant challenge for the clinician. We present a young patient with a very unusual presentation of Dementia with Lewy Bodies. The lack of motor symptoms and his marked apathy delayed his diagnosis. His symptoms were thought to be due to depression based on normal structural imaging and the psychiatric nature of his presentation. An extensive work-up was performed. Evidence of a structural neurodegenerative process was provided by the HMPAO-SPECT. Cardiac MIBG confirmed the diagnosis.

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来源期刊

Neurocase 医学-精神病学

CiteScore

1.40

自引率

12.50%

发文量

审稿时长

6-12 weeks

期刊介绍： Neurocase is a rapid response journal of case studies and innovative group studies in neuropsychology, neuropsychiatry and behavioral neurology that speak to the neural basis of cognition. Four types of manuscript are considered for publication: single case investigations that bear directly on issues of relevance to theoretical issues or brain-behavior relationships; group studies of subjects with brain dysfunction that address issues relevant to the understanding of human cognition; reviews of important topics in the domains of neuropsychology, neuropsychiatry and behavioral neurology; and brief reports (up to 2500 words) that replicate previous reports dealing with issues of considerable significance. Of particular interest are investigations that include precise anatomical localization of lesions or neural activity via imaging or other techniques, as well as studies of patients with neurodegenerative diseases, since these diseases are becoming more common as our population ages. Topic reviews are included in most issues.