胆道闭锁的门板和胆囊处的透明软骨。

Q4 Medicine

Autopsy and Case Reports Pub Date : 2024-04-04 eCollection Date: 2024-01-01 DOI:10.4322/acr.2024.481

Sangamitra Rajasekaran, Hari Neupane, Monika Bawa, Uma Nahar Saikia, Sadhna Lal, Suvradeep Mitra

{"title":"胆道闭锁的门板和胆囊处的透明软骨。","authors":"Sangamitra Rajasekaran, Hari Neupane, Monika Bawa, Uma Nahar Saikia, Sadhna Lal, Suvradeep Mitra","doi":"10.4322/acr.2024.481","DOIUrl":null,"url":null,"abstract":"Biliary atresia (BA) is a fibro-obliterative cholestatic disease of infancy. The presence of cartilage in the resected tissue is an uncommon finding. We documented the presence of both mature and immature hyaline cartilage in the portal plate and the wall of the gallbladder in a 2-month-old girl infant with BA who had undergone Kasai portoenterostomy. The presence of cartilage could be part of a heterotopia or an uncommon connective tissue metaplasia. The presence of immature cartilage with the merging of the perichondrium with the soft tissue highlights a metaplastic etiology in the index case.","PeriodicalId":53117,"journal":{"name":"Autopsy and Case Reports","volume":"14 ","pages":"e2024481"},"PeriodicalIF":0.0000,"publicationDate":"2024-04-04","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC11021023/pdf/","citationCount":"0","resultStr":"{\"title\":\"Hyaline cartilage at the portal plate and gallbladder in biliary atresia.\",\"authors\":\"Sangamitra Rajasekaran, Hari Neupane, Monika Bawa, Uma Nahar Saikia, Sadhna Lal, Suvradeep Mitra\",\"doi\":\"10.4322/acr.2024.481\",\"DOIUrl\":null,\"url\":null,\"abstract\":\"Biliary atresia (BA) is a fibro-obliterative cholestatic disease of infancy. The presence of cartilage in the resected tissue is an uncommon finding. We documented the presence of both mature and immature hyaline cartilage in the portal plate and the wall of the gallbladder in a 2-month-old girl infant with BA who had undergone Kasai portoenterostomy. The presence of cartilage could be part of a heterotopia or an uncommon connective tissue metaplasia. The presence of immature cartilage with the merging of the perichondrium with the soft tissue highlights a metaplastic etiology in the index case.\",\"PeriodicalId\":53117,\"journal\":{\"name\":\"Autopsy and Case Reports\",\"volume\":\"14 \",\"pages\":\"e2024481\"},\"PeriodicalIF\":0.0000,\"publicationDate\":\"2024-04-04\",\"publicationTypes\":\"Journal Article\",\"fieldsOfStudy\":null,\"isOpenAccess\":false,\"openAccessPdf\":\"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC11021023/pdf/\",\"citationCount\":\"0\",\"resultStr\":null,\"platform\":\"Semanticscholar\",\"paperid\":null,\"PeriodicalName\":\"Autopsy and Case Reports\",\"FirstCategoryId\":\"1085\",\"ListUrlMain\":\"https://doi.org/10.4322/acr.2024.481\",\"RegionNum\":0,\"RegionCategory\":null,\"ArticlePicture\":[],\"TitleCN\":null,\"AbstractTextCN\":null,\"PMCID\":null,\"EPubDate\":\"2024/1/1 0:00:00\",\"PubModel\":\"eCollection\",\"JCR\":\"Q4\",\"JCRName\":\"Medicine\",\"Score\":null,\"Total\":0}","platform":"Semanticscholar","paperid":null,"PeriodicalName":"Autopsy and Case Reports","FirstCategoryId":"1085","ListUrlMain":"https://doi.org/10.4322/acr.2024.481","RegionNum":0,"RegionCategory":null,"ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"2024/1/1 0:00:00","PubModel":"eCollection","JCR":"Q4","JCRName":"Medicine","Score":null,"Total":0}

引用次数: 0

摘要

胆道闭锁（BA）是一种婴儿期纤维盲性胆汁淤积症。在切除的组织中发现软骨并不常见。我们记录了一名 2 个月大的 BA 女婴的门板和胆囊壁上同时存在成熟和不成熟的透明软骨，她曾接受过葛西氏肠门造口术。软骨的存在可能是异位瘤或不常见的结缔组织增生的一部分。在该病例中，未成熟软骨的存在以及软骨周围与软组织的合并凸显了变构病的病因。

本文章由计算机程序翻译，如有差异，请以英文原文为准。

查看原文本刊更多论文

Hyaline cartilage at the portal plate and gallbladder in biliary atresia.

Biliary atresia (BA) is a fibro-obliterative cholestatic disease of infancy. The presence of cartilage in the resected tissue is an uncommon finding. We documented the presence of both mature and immature hyaline cartilage in the portal plate and the wall of the gallbladder in a 2-month-old girl infant with BA who had undergone Kasai portoenterostomy. The presence of cartilage could be part of a heterotopia or an uncommon connective tissue metaplasia. The presence of immature cartilage with the merging of the perichondrium with the soft tissue highlights a metaplastic etiology in the index case.

求助全文

通过发布文献求助，成功后即可免费获取论文全文。去求助

来源期刊

Autopsy and Case Reports Medicine-Internal Medicine

CiteScore

1.20

自引率

0.00%

发文量

审稿时长

9 weeks