定义路易体:在定义和概念不断变化的山坡上奔跑。

IF 4 3区 医学 Q2 NEUROSCIENCES
Tim E Moors, Dragomir Milovanovic
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引用次数: 0

摘要

路易体(LBs)是帕金森病和路易体痴呆症的病理标志,其特征是大脑中α-突触核蛋白(αSyn)蛋白的堆积。尽管路易体早在一个世纪前就被首次描述,但人们对其形成和形态发生机制的了解仍然不够全面。在此,我们对枸杞内含物的定义进行了历史性概述,并强调了在描述脑内含物时语义清晰和定义准确的重要性。最近成像技术的突破揭示了LB亚群的共同特征以及这些结构中膜结合细胞器的富集,从而对传统的LB形成模型提出了挑战。我们讨论了新出现的液-液相分离概念,即生物分子从溶液中分离出来形成致密凝聚体,并将其作为一种潜在的枸杞内含物形成机制。最后,我们强调需要根据形态特征和检测方案对枸杞进行操作性定义,尤其是在研究枸杞形成机制时。更好地了解LB的组织和超微结构有助于开发针对突触核蛋白病的靶向治疗策略。
本文章由计算机程序翻译,如有差异,请以英文原文为准。
Defining a Lewy Body: Running Up the Hill of Shifting Definitions and Evolving Concepts.

Lewy bodies (LBs) are pathological hallmarks of Parkinson's disease and dementia with Lewy bodies, characterized by the accumulation of α-synuclein (αSyn) protein in the brain. While LBs were first described a century ago, their formation and morphogenesis mechanisms remain incompletely understood. Here, we present a historical overview of LB definitions and highlight the importance of semantic clarity and precise definitions when describing brain inclusions. Recent breakthroughs in imaging revealed shared features within LB subsets and the enrichment of membrane-bound organelles in these structures, challenging the conventional LB formation model. We discuss the involvement of emerging concepts of liquid-liquid phase separation, where biomolecules demix from a solution to form dense condensates, as a potential LB formation mechanism. Finally, we emphasize the need for the operational definitions of LBs based on morphological characteristics and detection protocols, particularly in studies investigating LB formation mechanisms. A better understanding of LB organization and ultrastructure can contribute to the development of targeted therapeutic strategies for synucleinopathies.

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来源期刊
CiteScore
8.40
自引率
5.80%
发文量
338
审稿时长
>12 weeks
期刊介绍: The Journal of Parkinson''s Disease (JPD) publishes original research in basic science, translational research and clinical medicine in Parkinson’s disease in cooperation with the Journal of Alzheimer''s Disease. It features a first class Editorial Board and provides rigorous peer review and rapid online publication.
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