原发性脊髓硬膜内髓外尤文氏肉瘤/周围神经外胚层肿瘤临床伪装为神经源性肿瘤1例报告及文献复习

IF 1.8 Q4 NEUROSCIENCES
B. K. Praveen, Saikat Das, Manish Gupta, Deepti Joshi, Hemlata Panwar
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引用次数: 0

摘要

尤文氏肉瘤(ES)/周围神经外胚层肿瘤(pPNET)是一种罕见的、高度恶性的、未分化的、起源于神经外胚层的原始圆细胞肿瘤。很少观察到pPNETs累及脊柱,脊髓硬膜内髓外骨外原发性ES/pPNET极为罕见。我们报告一个23岁的男性病例,主诉腰痛和髋关节疼痛放射到左侧腹股沟区域四个月。影像学表现提示为神经源性肿瘤。进行细胞形态学、组织形态学及免疫组化评价。诊断符合ES/pPNET。临床病史、细胞形态学、组织病理学、免疫组织化学和分子分析之间的密切联系有助于将原发性脊柱ES/PNET与其他原发性脊柱肿瘤区分开来,并有助于临床医生尽早开始治疗。
本文章由计算机程序翻译,如有差异,请以英文原文为准。
Primary Spinal Intradural Extramedullary Ewing’s Sarcoma/Peripheral Neuroectodermal Tumour Masquerading Clinically as a Neurogenic Tumour: A Case Report and Review of Literature
Ewing’s Sarcomas (ES)/Peripheral neuroectodermal tumour (pPNET) are heterogenous group of rare, highly malignant, undifferentiated primitive round-cell neoplasms of neuroectodermal origin. pPNETs are seldom observed to involve the spine of which Spinal Intradural Extramedullary Extraosseous Primary ES/pPNET are extremely rare. We report a case of a 23-year-old male with complaints of low backache and hip pain radiating to the left inguinal region for four months. Radiology findings were suggestive of a neurogenic tumour. Cytomorphology, histomorphology and immunohistochemistry evaluation were done. Diagnosis was consistent with ES/pPNET. Careful correlation between clinical history, cytomorphology, histopathology, immunohistochemical and molecular analysis can help to distinguish primary spinal ES/PNET from other primary spinal tumours and will help clinicians to start treatment at the earliest.
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来源期刊
Annals of Neurosciences
Annals of Neurosciences NEUROSCIENCES-
CiteScore
2.40
自引率
0.00%
发文量
39
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