{"title":"特殊治疗后恢复良好的多发性硬化症:Susac综合征","authors":"Torri Clerici Valentina, Bianchi-Marzoli Stefania","doi":"10.47363/jorrr/2021(2)112","DOIUrl":null,"url":null,"abstract":"Susac Syndrome (SuS) is a rare disease, characterized by an autoimmune endothelopathy, that involves brain, retina and inner ear. We describe a case of a young woman affected by inner ear-predominant SuS, initially suspected for demyelinating disease, with delayed diagnosis and irreversible hearing ischemic damage, but good prognosis, treated according to current recommendations","PeriodicalId":373984,"journal":{"name":"Journal of Ophthalmology Research Reviews & Reports","volume":"16 1","pages":"0"},"PeriodicalIF":0.0000,"publicationDate":"2021-06-30","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":"0","resultStr":"{\"title\":\"A Multiple Sclerosis Mimiker with Good Recovery following Specific Therapy: Susac Syndrome\",\"authors\":\"Torri Clerici Valentina, Bianchi-Marzoli Stefania\",\"doi\":\"10.47363/jorrr/2021(2)112\",\"DOIUrl\":null,\"url\":null,\"abstract\":\"Susac Syndrome (SuS) is a rare disease, characterized by an autoimmune endothelopathy, that involves brain, retina and inner ear. We describe a case of a young woman affected by inner ear-predominant SuS, initially suspected for demyelinating disease, with delayed diagnosis and irreversible hearing ischemic damage, but good prognosis, treated according to current recommendations\",\"PeriodicalId\":373984,\"journal\":{\"name\":\"Journal of Ophthalmology Research Reviews & Reports\",\"volume\":\"16 1\",\"pages\":\"0\"},\"PeriodicalIF\":0.0000,\"publicationDate\":\"2021-06-30\",\"publicationTypes\":\"Journal Article\",\"fieldsOfStudy\":null,\"isOpenAccess\":false,\"openAccessPdf\":\"\",\"citationCount\":\"0\",\"resultStr\":null,\"platform\":\"Semanticscholar\",\"paperid\":null,\"PeriodicalName\":\"Journal of Ophthalmology Research Reviews & Reports\",\"FirstCategoryId\":\"1085\",\"ListUrlMain\":\"https://doi.org/10.47363/jorrr/2021(2)112\",\"RegionNum\":0,\"RegionCategory\":null,\"ArticlePicture\":[],\"TitleCN\":null,\"AbstractTextCN\":null,\"PMCID\":null,\"EPubDate\":\"\",\"PubModel\":\"\",\"JCR\":\"\",\"JCRName\":\"\",\"Score\":null,\"Total\":0}","platform":"Semanticscholar","paperid":null,"PeriodicalName":"Journal of Ophthalmology Research Reviews & Reports","FirstCategoryId":"1085","ListUrlMain":"https://doi.org/10.47363/jorrr/2021(2)112","RegionNum":0,"RegionCategory":null,"ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"","PubModel":"","JCR":"","JCRName":"","Score":null,"Total":0}
A Multiple Sclerosis Mimiker with Good Recovery following Specific Therapy: Susac Syndrome
Susac Syndrome (SuS) is a rare disease, characterized by an autoimmune endothelopathy, that involves brain, retina and inner ear. We describe a case of a young woman affected by inner ear-predominant SuS, initially suspected for demyelinating disease, with delayed diagnosis and irreversible hearing ischemic damage, but good prognosis, treated according to current recommendations