A curious case of classic biphasic pulmonary blastoma

Classic biphasic pulmonary blastoma is an uncommon and highly aggressive primary pulmonary malignancy characteristically arising from fetal lung tissues comprising biphasic histology that is made up of both epithelial and mesenchymal components. We present this rare case in which a young adult presented with chest pain for 3 months and dyspnea for 1 month. Contrast-enhanced computed tomography of the thorax revealed a right-sided homogeneous mass. The diagnosis was confirmed by transthoracic biopsy and histopathological examination. Surgical excision remains the treatment of choice. Recurrence usually occurs within 12 months of surgery, with 5-year survival rates <20%. We report this rare malignancy with a special focus on improving the management of this malignancy.