伯基特的细胞淋巴瘤在女孩的卵巢里。临床案例

Л. В. Адамян, Елена Викторовна Сибирская, С А Короткова, Г. Т. Осипова, Г. М. Тургунова, Л. Г. Пивазян
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引用次数: 0

摘要

脾b细胞边缘区淋巴瘤伴明显浆细胞分化:Mott细胞的肿瘤变体?脾b细胞边缘带淋巴瘤(SMZL)——一种罕见的b细胞非霍奇金淋巴瘤,形态学上以成熟淋巴样细胞为代表,免疫学特征上与次级滤泡边缘带淋巴细胞相对应。浆细胞分化可以在边缘区淋巴瘤中发生,但我们描述了一例脾脏b细胞边缘区淋巴瘤中大量的莫特细胞作为肿瘤底物。我们报告了第一例以莫特细胞为代表的SMZL。这是俄罗斯报道的第二例莫特细胞瘤。这是收集的脾淋巴瘤资料中唯一的一例。形态学模式的特点是单克隆淋巴样细胞明显增殖,浆细胞分化,存在莫特细胞,这是细胞内强烈分泌免疫球蛋白的证据。
本文章由计算机程序翻译,如有差异,请以英文原文为准。
В-клеточная лимфома беркитта в яичниках у девочки. Клинический случай
Splenic B-cell marginal zone lymphoma with marked plasmocytic differentiation: tumor variant from Mott cells? Splenic B-cell marginal zone lymphoma (SMZL) – a rare B-cell non-Hodgkin,s lymphoma, which is represented morphologically by ma-ture lymphoid cells, corresponding to lymphocytes of secondary follicles marginal zone by immunological characteristics. Plasma cell differentiation can be in marginal zone lymphoma, but we described a single case of abundance of Mott cells as a tumor substrate in splenic B-cell marginal zone lymphoma. We present the first case of SMZL represented by Mott cells. This was the second case of Mott cells tumor described in Russia. This observation is the only case among the collected material of splenic lymphomas. The morphological pattern is characterized by marked proliferation of monoclonal lymphoid cells with plasma cell differentiation with presence of Mott cells and is evidence of intense intracellular secretion of immunoglobulins.
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