{"title":"免疫球蛋白治疗浆液水肿伴感觉运动轴突多发性神经病1例","authors":"R. Jagdish","doi":"10.18231/j.agems.2022.008","DOIUrl":null,"url":null,"abstract":"Sleromyxedema is a rare disease characterised by extensive mucin deposition with fibrosis in dermis. It is often associated with monoclonal gammopathy. Its true prevalence and/or cause is unknown due to its rarity. Various extra-cutaneous manifestations can be associated with sleromyxedema such as dermoneuro syndrome, neuropathy, rheumatological problems or various malignancies. This case report showed that a patient with sleromyxedema and neuropathy had positive outcomes when treated with intravenous immunoglobulin (IVIg) and steroids pulses. The underlying cause of the patient’s condition was unknown.","PeriodicalId":129502,"journal":{"name":"Annals of Geriatric Education and Medical Sciences","volume":"87 1","pages":"0"},"PeriodicalIF":0.0000,"publicationDate":"2022-07-15","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":"0","resultStr":"{\"title\":\"Case report of Sleromyxedema with sensory motor axonal polyneuropathy treated with immunoglobulin therapy\",\"authors\":\"R. Jagdish\",\"doi\":\"10.18231/j.agems.2022.008\",\"DOIUrl\":null,\"url\":null,\"abstract\":\"Sleromyxedema is a rare disease characterised by extensive mucin deposition with fibrosis in dermis. It is often associated with monoclonal gammopathy. Its true prevalence and/or cause is unknown due to its rarity. Various extra-cutaneous manifestations can be associated with sleromyxedema such as dermoneuro syndrome, neuropathy, rheumatological problems or various malignancies. This case report showed that a patient with sleromyxedema and neuropathy had positive outcomes when treated with intravenous immunoglobulin (IVIg) and steroids pulses. The underlying cause of the patient’s condition was unknown.\",\"PeriodicalId\":129502,\"journal\":{\"name\":\"Annals of Geriatric Education and Medical Sciences\",\"volume\":\"87 1\",\"pages\":\"0\"},\"PeriodicalIF\":0.0000,\"publicationDate\":\"2022-07-15\",\"publicationTypes\":\"Journal Article\",\"fieldsOfStudy\":null,\"isOpenAccess\":false,\"openAccessPdf\":\"\",\"citationCount\":\"0\",\"resultStr\":null,\"platform\":\"Semanticscholar\",\"paperid\":null,\"PeriodicalName\":\"Annals of Geriatric Education and Medical Sciences\",\"FirstCategoryId\":\"1085\",\"ListUrlMain\":\"https://doi.org/10.18231/j.agems.2022.008\",\"RegionNum\":0,\"RegionCategory\":null,\"ArticlePicture\":[],\"TitleCN\":null,\"AbstractTextCN\":null,\"PMCID\":null,\"EPubDate\":\"\",\"PubModel\":\"\",\"JCR\":\"\",\"JCRName\":\"\",\"Score\":null,\"Total\":0}","platform":"Semanticscholar","paperid":null,"PeriodicalName":"Annals of Geriatric Education and Medical Sciences","FirstCategoryId":"1085","ListUrlMain":"https://doi.org/10.18231/j.agems.2022.008","RegionNum":0,"RegionCategory":null,"ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"","PubModel":"","JCR":"","JCRName":"","Score":null,"Total":0}
Case report of Sleromyxedema with sensory motor axonal polyneuropathy treated with immunoglobulin therapy
Sleromyxedema is a rare disease characterised by extensive mucin deposition with fibrosis in dermis. It is often associated with monoclonal gammopathy. Its true prevalence and/or cause is unknown due to its rarity. Various extra-cutaneous manifestations can be associated with sleromyxedema such as dermoneuro syndrome, neuropathy, rheumatological problems or various malignancies. This case report showed that a patient with sleromyxedema and neuropathy had positive outcomes when treated with intravenous immunoglobulin (IVIg) and steroids pulses. The underlying cause of the patient’s condition was unknown.