免疫球蛋白治疗浆液水肿伴感觉运动轴突多发性神经病1例

R. Jagdish
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引用次数: 0

摘要

浆液性水肿是一种罕见的疾病,其特征是真皮内广泛的粘蛋白沉积伴纤维化。它通常与单克隆γ病有关。由于其罕见,其真正流行和/或原因尚不清楚。各种皮肤外表现可与浆液性水肿有关,如真皮综合征、神经病变、风湿病或各种恶性肿瘤。本病例报告显示,静脉注射免疫球蛋白(IVIg)和类固醇脉冲治疗的浆液性水肿和神经病变患者有积极的结果。患者病情的根本原因尚不清楚。
本文章由计算机程序翻译,如有差异,请以英文原文为准。
Case report of Sleromyxedema with sensory motor axonal polyneuropathy treated with immunoglobulin therapy
Sleromyxedema is a rare disease characterised by extensive mucin deposition with fibrosis in dermis. It is often associated with monoclonal gammopathy. Its true prevalence and/or cause is unknown due to its rarity. Various extra-cutaneous manifestations can be associated with sleromyxedema such as dermoneuro syndrome, neuropathy, rheumatological problems or various malignancies. This case report showed that a patient with sleromyxedema and neuropathy had positive outcomes when treated with intravenous immunoglobulin (IVIg) and steroids pulses. The underlying cause of the patient’s condition was unknown.
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