{"title":"Hippel-Lindau疾病。1例家庭病史。","authors":"M A Feldberg, P F van Waes, D H Schönfeld","doi":"","DOIUrl":null,"url":null,"abstract":"<p><p>This article describes the results of a prospective study in the 4 asymptomatic members of a family affected with Hippel-Lindau disease after the death of 2 patients and the surgical findings of the third. It stresses the multicentric and bilateral origin of renal cell carcinoma in Hippel-Lindau disease, usually combined with renal cortical cysts. The walls of these cysts often contain carcinoma cells. It is important that all relatives of a patient with the Hippel-Lindau disease are adequately screened.</p>","PeriodicalId":76405,"journal":{"name":"Radiologia clinica","volume":"47 2","pages":"91-9"},"PeriodicalIF":0.0000,"publicationDate":"1978-01-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":"0","resultStr":"{\"title\":\"Hippel-Lindau disease. A case history of one family.\",\"authors\":\"M A Feldberg, P F van Waes, D H Schönfeld\",\"doi\":\"\",\"DOIUrl\":null,\"url\":null,\"abstract\":\"<p><p>This article describes the results of a prospective study in the 4 asymptomatic members of a family affected with Hippel-Lindau disease after the death of 2 patients and the surgical findings of the third. It stresses the multicentric and bilateral origin of renal cell carcinoma in Hippel-Lindau disease, usually combined with renal cortical cysts. The walls of these cysts often contain carcinoma cells. It is important that all relatives of a patient with the Hippel-Lindau disease are adequately screened.</p>\",\"PeriodicalId\":76405,\"journal\":{\"name\":\"Radiologia clinica\",\"volume\":\"47 2\",\"pages\":\"91-9\"},\"PeriodicalIF\":0.0000,\"publicationDate\":\"1978-01-01\",\"publicationTypes\":\"Journal Article\",\"fieldsOfStudy\":null,\"isOpenAccess\":false,\"openAccessPdf\":\"\",\"citationCount\":\"0\",\"resultStr\":null,\"platform\":\"Semanticscholar\",\"paperid\":null,\"PeriodicalName\":\"Radiologia clinica\",\"FirstCategoryId\":\"1085\",\"ListUrlMain\":\"\",\"RegionNum\":0,\"RegionCategory\":null,\"ArticlePicture\":[],\"TitleCN\":null,\"AbstractTextCN\":null,\"PMCID\":null,\"EPubDate\":\"\",\"PubModel\":\"\",\"JCR\":\"\",\"JCRName\":\"\",\"Score\":null,\"Total\":0}","platform":"Semanticscholar","paperid":null,"PeriodicalName":"Radiologia clinica","FirstCategoryId":"1085","ListUrlMain":"","RegionNum":0,"RegionCategory":null,"ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"","PubModel":"","JCR":"","JCRName":"","Score":null,"Total":0}
Hippel-Lindau disease. A case history of one family.
This article describes the results of a prospective study in the 4 asymptomatic members of a family affected with Hippel-Lindau disease after the death of 2 patients and the surgical findings of the third. It stresses the multicentric and bilateral origin of renal cell carcinoma in Hippel-Lindau disease, usually combined with renal cortical cysts. The walls of these cysts often contain carcinoma cells. It is important that all relatives of a patient with the Hippel-Lindau disease are adequately screened.