Hyoiru Kim, H. Koh, K. Chung, J. Oh, Young Nyun Park, M. J. Kim
{"title":"Alagille综合征合并肝管闭锁1例","authors":"Hyoiru Kim, H. Koh, K. Chung, J. Oh, Young Nyun Park, M. J. Kim","doi":"10.5223/KJPGN.2008.11.1.65","DOIUrl":null,"url":null,"abstract":"A two-month-old baby had acholic stool, neonatal hyperbilirubinemia and congenital heart disease. Atresia of the hepatic duct was confirmed by open cholangiography, which showed a non-opacified intrahepatic bile duct. Liver biopsy and the Kasai operation were performed. Because the liver biopsy pathology revealed a paucity of intrahepatic bile ducts, the patient was diagnosed with the Alagille syndrome. We report the case of an infant diagnosed with the Alagille syndrome with atresia of the hepatic duct. (Korean J Pediatr Gastroenterol Nutr 2008; 11: 65∼69)","PeriodicalId":212346,"journal":{"name":"Korean Journal of Pediatric Gastroenterology and Nutrition","volume":"86 1","pages":"0"},"PeriodicalIF":0.0000,"publicationDate":"2008-03-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":"0","resultStr":"{\"title\":\"A Case of Alagille Syndrome with Atresia of the Hepatic Duct\",\"authors\":\"Hyoiru Kim, H. Koh, K. Chung, J. Oh, Young Nyun Park, M. J. Kim\",\"doi\":\"10.5223/KJPGN.2008.11.1.65\",\"DOIUrl\":null,\"url\":null,\"abstract\":\"A two-month-old baby had acholic stool, neonatal hyperbilirubinemia and congenital heart disease. Atresia of the hepatic duct was confirmed by open cholangiography, which showed a non-opacified intrahepatic bile duct. Liver biopsy and the Kasai operation were performed. Because the liver biopsy pathology revealed a paucity of intrahepatic bile ducts, the patient was diagnosed with the Alagille syndrome. We report the case of an infant diagnosed with the Alagille syndrome with atresia of the hepatic duct. (Korean J Pediatr Gastroenterol Nutr 2008; 11: 65∼69)\",\"PeriodicalId\":212346,\"journal\":{\"name\":\"Korean Journal of Pediatric Gastroenterology and Nutrition\",\"volume\":\"86 1\",\"pages\":\"0\"},\"PeriodicalIF\":0.0000,\"publicationDate\":\"2008-03-01\",\"publicationTypes\":\"Journal Article\",\"fieldsOfStudy\":null,\"isOpenAccess\":false,\"openAccessPdf\":\"\",\"citationCount\":\"0\",\"resultStr\":null,\"platform\":\"Semanticscholar\",\"paperid\":null,\"PeriodicalName\":\"Korean Journal of Pediatric Gastroenterology and Nutrition\",\"FirstCategoryId\":\"1085\",\"ListUrlMain\":\"https://doi.org/10.5223/KJPGN.2008.11.1.65\",\"RegionNum\":0,\"RegionCategory\":null,\"ArticlePicture\":[],\"TitleCN\":null,\"AbstractTextCN\":null,\"PMCID\":null,\"EPubDate\":\"\",\"PubModel\":\"\",\"JCR\":\"\",\"JCRName\":\"\",\"Score\":null,\"Total\":0}","platform":"Semanticscholar","paperid":null,"PeriodicalName":"Korean Journal of Pediatric Gastroenterology and Nutrition","FirstCategoryId":"1085","ListUrlMain":"https://doi.org/10.5223/KJPGN.2008.11.1.65","RegionNum":0,"RegionCategory":null,"ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"","PubModel":"","JCR":"","JCRName":"","Score":null,"Total":0}
A Case of Alagille Syndrome with Atresia of the Hepatic Duct
A two-month-old baby had acholic stool, neonatal hyperbilirubinemia and congenital heart disease. Atresia of the hepatic duct was confirmed by open cholangiography, which showed a non-opacified intrahepatic bile duct. Liver biopsy and the Kasai operation were performed. Because the liver biopsy pathology revealed a paucity of intrahepatic bile ducts, the patient was diagnosed with the Alagille syndrome. We report the case of an infant diagnosed with the Alagille syndrome with atresia of the hepatic duct. (Korean J Pediatr Gastroenterol Nutr 2008; 11: 65∼69)
求助内容：
应助结果提醒方式：
京公网安备 11010802042870号
