左室非压实性心肌病

N. Oryshchyn, Y. Ivaniv
{"title":"左室非压实性心肌病","authors":"N. Oryshchyn, Y. Ivaniv","doi":"10.25040/ntsh2019.01.07","DOIUrl":null,"url":null,"abstract":"Introduction. Left ventricular non-compaction (LVNC) is a rare form of cardiomyopathy, congenital defect of the intrauterine process of ventricular embryogenesis. The main feature of this pathology is an existence of prominent trabeculations in the left ventricle and deep intertrabecular recesses. The pathological structure of the myocardium leads to its dilatation and dysfunction, heart failure symptoms, embolic episodes and arrhythmia. \nThe aim of the manuscript is to present a spectrum of clinical manifestations of left ventricular non-compaction (LVNC). \nMaterials and methods Patients were diagnosed and treated in The Lviv Centre of Cardiology. Two of them were admitted for heart failure symptoms, in one patient with dysrhythmia and left bundle brunch block (LBBB); and one patient had non-specific chest pain. Cardiac imaging with echocardiography and MRI were performed. \nResults. Echocardiography revealed criteria of LVNC in all patient, in two of them the diagnosis was confirmed by cardiac MRI. Patients with heart failure symptoms were managed with optimal medical therapy, CRT-D has been implanted in patient with LBBB. Asymptomatic patient is under follow-up. \nConclusions. LVNC is a cardiomyopathy with distinct echocardiographic and MRI-features and wide spectrum of clinical presentations. The prognosis in case of LVNC is serious due to systolic LV dysfunction, cardiac arrhythmia and embolic events. Echocardiography is a diagnostic tool to identify LVNC, cardiac MRI confirms the diagnosis of LVNC if echocardiography data is insufficient.","PeriodicalId":140699,"journal":{"name":"Proceedings of the Shevchenko Scientific Society. Medical Sciences","volume":"1 1","pages":"0"},"PeriodicalIF":0.0000,"publicationDate":"2019-06-24","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"","citationCount":"2","resultStr":"{\"title\":\"LEFT VENTRICULAR NON-COMPACTION CARDIOMYOPATHY\",\"authors\":\"N. Oryshchyn, Y. Ivaniv\",\"doi\":\"10.25040/ntsh2019.01.07\",\"DOIUrl\":null,\"url\":null,\"abstract\":\"Introduction. Left ventricular non-compaction (LVNC) is a rare form of cardiomyopathy, congenital defect of the intrauterine process of ventricular embryogenesis. The main feature of this pathology is an existence of prominent trabeculations in the left ventricle and deep intertrabecular recesses. The pathological structure of the myocardium leads to its dilatation and dysfunction, heart failure symptoms, embolic episodes and arrhythmia. \\nThe aim of the manuscript is to present a spectrum of clinical manifestations of left ventricular non-compaction (LVNC). \\nMaterials and methods Patients were diagnosed and treated in The Lviv Centre of Cardiology. Two of them were admitted for heart failure symptoms, in one patient with dysrhythmia and left bundle brunch block (LBBB); and one patient had non-specific chest pain. Cardiac imaging with echocardiography and MRI were performed. \\nResults. Echocardiography revealed criteria of LVNC in all patient, in two of them the diagnosis was confirmed by cardiac MRI. Patients with heart failure symptoms were managed with optimal medical therapy, CRT-D has been implanted in patient with LBBB. Asymptomatic patient is under follow-up. \\nConclusions. LVNC is a cardiomyopathy with distinct echocardiographic and MRI-features and wide spectrum of clinical presentations. The prognosis in case of LVNC is serious due to systolic LV dysfunction, cardiac arrhythmia and embolic events. Echocardiography is a diagnostic tool to identify LVNC, cardiac MRI confirms the diagnosis of LVNC if echocardiography data is insufficient.\",\"PeriodicalId\":140699,\"journal\":{\"name\":\"Proceedings of the Shevchenko Scientific Society. Medical Sciences\",\"volume\":\"1 1\",\"pages\":\"0\"},\"PeriodicalIF\":0.0000,\"publicationDate\":\"2019-06-24\",\"publicationTypes\":\"Journal Article\",\"fieldsOfStudy\":null,\"isOpenAccess\":false,\"openAccessPdf\":\"\",\"citationCount\":\"2\",\"resultStr\":null,\"platform\":\"Semanticscholar\",\"paperid\":null,\"PeriodicalName\":\"Proceedings of the Shevchenko Scientific Society. Medical Sciences\",\"FirstCategoryId\":\"1085\",\"ListUrlMain\":\"https://doi.org/10.25040/ntsh2019.01.07\",\"RegionNum\":0,\"RegionCategory\":null,\"ArticlePicture\":[],\"TitleCN\":null,\"AbstractTextCN\":null,\"PMCID\":null,\"EPubDate\":\"\",\"PubModel\":\"\",\"JCR\":\"\",\"JCRName\":\"\",\"Score\":null,\"Total\":0}","platform":"Semanticscholar","paperid":null,"PeriodicalName":"Proceedings of the Shevchenko Scientific Society. Medical Sciences","FirstCategoryId":"1085","ListUrlMain":"https://doi.org/10.25040/ntsh2019.01.07","RegionNum":0,"RegionCategory":null,"ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"","PubModel":"","JCR":"","JCRName":"","Score":null,"Total":0}
引用次数: 2

摘要

介绍。左心室不压实是一种罕见的心肌病,是室性胚胎发生过程中的先天性缺陷。这种病理的主要特征是左心室存在明显的小梁和深小梁间窝。心肌的病理结构导致其扩张和功能障碍,心衰症状,栓塞发作和心律失常。该手稿的目的是提出一个频谱的临床表现的左心室不压实(LVNC)。材料和方法患者在利沃夫心脏病中心诊断和治疗。其中两名患者因心力衰竭症状入院,其中一名患者伴有心律失常和左束早午餐阻滞(LBBB);一名患者有非特异性胸痛。行超声心动图和MRI心脏显像。结果。所有患者超声心动图均显示LVNC的诊断标准,其中2例经心脏MRI证实。对出现心衰症状的患者进行最佳药物治疗,CRT-D已植入LBBB患者。无症状患者正在随访中。结论。LVNC是一种心肌病具有独特的超声心动图和mri特征和广泛的临床表现。LVNC的预后因收缩期左室功能障碍、心律失常和栓塞事件而严重。超声心动图是鉴别LVNC的诊断工具,如果超声心动图资料不足,心脏MRI可证实LVNC的诊断。
本文章由计算机程序翻译,如有差异,请以英文原文为准。
LEFT VENTRICULAR NON-COMPACTION CARDIOMYOPATHY
Introduction. Left ventricular non-compaction (LVNC) is a rare form of cardiomyopathy, congenital defect of the intrauterine process of ventricular embryogenesis. The main feature of this pathology is an existence of prominent trabeculations in the left ventricle and deep intertrabecular recesses. The pathological structure of the myocardium leads to its dilatation and dysfunction, heart failure symptoms, embolic episodes and arrhythmia. The aim of the manuscript is to present a spectrum of clinical manifestations of left ventricular non-compaction (LVNC). Materials and methods Patients were diagnosed and treated in The Lviv Centre of Cardiology. Two of them were admitted for heart failure symptoms, in one patient with dysrhythmia and left bundle brunch block (LBBB); and one patient had non-specific chest pain. Cardiac imaging with echocardiography and MRI were performed. Results. Echocardiography revealed criteria of LVNC in all patient, in two of them the diagnosis was confirmed by cardiac MRI. Patients with heart failure symptoms were managed with optimal medical therapy, CRT-D has been implanted in patient with LBBB. Asymptomatic patient is under follow-up. Conclusions. LVNC is a cardiomyopathy with distinct echocardiographic and MRI-features and wide spectrum of clinical presentations. The prognosis in case of LVNC is serious due to systolic LV dysfunction, cardiac arrhythmia and embolic events. Echocardiography is a diagnostic tool to identify LVNC, cardiac MRI confirms the diagnosis of LVNC if echocardiography data is insufficient.
求助全文
通过发布文献求助,成功后即可免费获取论文全文。 去求助
来源期刊
自引率
0.00%
发文量
0
×
引用
GB/T 7714-2015
复制
MLA
复制
APA
复制
导出至
BibTeX EndNote RefMan NoteFirst NoteExpress
×
提示
您的信息不完整,为了账户安全,请先补充。
现在去补充
×
提示
您因"违规操作"
具体请查看互助需知
我知道了
×
提示
确定
请完成安全验证×
copy
已复制链接
快去分享给好友吧!
我知道了
右上角分享
点击右上角分享
0
联系我们:info@booksci.cn Book学术提供免费学术资源搜索服务,方便国内外学者检索中英文文献。致力于提供最便捷和优质的服务体验。 Copyright © 2023 布克学术 All rights reserved.
京ICP备2023020795号-1
ghs 京公网安备 11010802042870号
Book学术文献互助
Book学术文献互助群
群 号:604180095
Book学术官方微信