抗mda5抗体阳性皮肌炎伴轻度脑病伴可逆性脾损害:可能的罕见关联?

IF 1.1 Q2 MEDICINE, GENERAL & INTERNAL

Wiener medizinische Wochenschrift Pub Date : 2023-09-01 DOI:10.1007/s10354-022-00943-0

Khadija Saghir, Mohammed Chraa, Najib Kissani, Hajar Joulal, Lamiaa Essaadouni, Nissrine Louhab

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引用次数: 0

摘要

在皮肌炎(DM)中很少观察到中枢神经系统(CNS)受累。然而，有非常罕见的病例报告中枢神经系统累及青少年皮肌炎。糖尿病脑病的发生可能有多种原因，如脑血管炎和低灌注/高血压性脑病，但主要是免疫抑制剂治疗的结果。我们在此首次报道一例患有两种罕见疾病的患者，即抗mda5抗体阳性皮肌炎和轻度脑病伴可逆性脾损害(MERS)。

本文章由计算机程序翻译，如有差异，请以英文原文为准。

Anti-MDA5 antibody-positive dermatomyositis with mild encephalopathy with reversible splenial lesion: a possible rare association?

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Anti-MDA5 antibody-positive dermatomyositis with mild encephalopathy with reversible splenial lesion: a possible rare association?

Central nervous system (CNS) involvement in dermatomyositis (DM) is seldom observed. However, there are very rare case reports of CNS involvement with juvenile dermatomyositis. Encephalopathy in DM may occur for a number of reasons, such as cerebral vasculitis and hypoperfusion/hypertensive encephalopathy, but mostly as a consequence of immunosuppressant treatment. We report here for the first time the case of a patient with two rare diseases, namely anti-MDA5 antibody-positive dermatomyositis and mild encephalopathy with reversible splenial lesion (MERS).

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来源期刊

Wiener medizinische Wochenschrift MEDICINE, GENERAL & INTERNAL-

CiteScore

2.50

自引率

0.00%

发文量

期刊介绍： ''From the microscope to clinical application!'', Scientists from all European countries make available their recent research results and practical experience through Wiener Medizinische Wochenschrift, the renowned English- and German-language forum. Both original articles and reviews on a broad spectrum of clinical and preclinical medicine are presented within the successful framework of thematic issues compiled by guest editors. Selected cutting-edge topics, such as dementia, geriatric oncology, Helicobacter pylori and phytomedicine make the journal a mandatory source of information.