胎儿体内的异常血管环

IF 1.5 4区医学 Q3 CARDIAC & CARDIOVASCULAR SYSTEMS

Pediatric Cardiology Pub Date : 2024-10-01 Epub Date: 2023-08-11 DOI:10.1007/s00246-023-03261-3

A Savis, C Oakley, M P M Van Poppel, D F A Lloyd, K Pushparajah, T V Vigneswaran, V Zidere

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引用次数: 0

摘要

我们介绍了两个患有异常血管环的胎儿的临床过程、超声心动图和遗传学发现，该血管环由带有右动脉导管的左主动脉弓和异常的右锁骨下动脉形成。一个胎儿被诊断为 22q11.2 微缺失，另一个在婴儿期出现症状。对于出现气管食管压迫症状而又伴有左主动脉弓的患者，考虑动脉导管韧带的位置非常重要。这些病例还强调，左主动脉弓形成的血管环可能与右主动脉弓形成的血管环有类似的关联。

本文章由计算机程序翻译，如有差异，请以英文原文为准。

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Unusual Vascular Ring in the Fetus.

We present the clinical course and echocardiographic and genetic findings of two fetuses with an unusual vascular ring, created by a left aortic arch with a right arterial duct and an aberrant right subclavian artery. One fetus was diagnosed with 22q11.2 microdeletion and the other became symptomatic in infancy. It is important to consider the position of the arterial ductal ligament in patients who present with tracheoesophageal compressive symptoms in the presence of a left aortic arch. These cases also highlight that a vascular ring formed from a left arch may have similar associations to a vascular ring formed by a right aortic arch.

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来源期刊

Pediatric Cardiology 医学-小儿科

CiteScore

3.30

自引率

6.20%

发文量

258

审稿时长

12 months

期刊介绍： The editor of Pediatric Cardiology welcomes original manuscripts concerning all aspects of heart disease in infants, children, and adolescents, including embryology and anatomy, physiology and pharmacology, biochemistry, pathology, genetics, radiology, clinical aspects, investigative cardiology, electrophysiology and echocardiography, and cardiac surgery. Articles which may include original articles, review articles, letters to the editor etc., must be written in English and must be submitted solely to Pediatric Cardiology.