Myxofibrosarcoma of Right Fronto-Temporal Region With Intracranial Extension: A case report

Abstract

Myxofibrosarcoma, is a myxoid variant of Malignant Fibrous Histiocytoma (MFH) first described by Weiss & Enzinger (1) with a better prognosis. MFH rarely occurs in the skull, with only 17 cases documented in literature (2). The tumor frequently erodes the outer table of the skull and spreads in the extracranial space. Intradural and brain invasion are very rare. We report a case of myxofibrosarcoma originating in the right fronto-temporal region with subsequent intracranial extension.