Microangiopathy of the Brain, Eyes and Ears: A Case Report

Abstract

Susac syndrome is a neurological condition which affects the brain, the eyes and the ears, hence presenting with a triad of encephalopathy, sensorineural hearing loss and branch retinal artery occlusion. It is a very rare condition. Only about 300 cases of Susac syndrome have been reported. It is theorized that Susac syndrome has an immunologic basis. This case report aims to add its share to the limited number of cases of Susac syndrome seen worldwide. This case report sheds light on a Caucasian woman diagnosed with Susac syndrome in West Virginia. The patient presented to the ER with syncope and altered mental status. The MRI showed multiple infarcts involving corpus callosum. Differential diagnoses were ruled out and she was started on intravenous methylprednisolone and intravenous immunoglobulin to treat her condition.