Inflammatory Fibrosarcoma: A Rare Tumour Entity Involving Retroperitoneum And Colon

Abstract

An inflammatory fibrosarcoma is a rare tumour with a varied biological behaviour, from benign to locally aggressive and occasionally malignant. It generally involves mesentery and retroperitoneal structures, but it rarely can involve the hollow viscera and commonly affects children and young adults. We report a case of inflammatory fibrosarcoma affecting an unusual age group, involving the ileo-caecal junction and ascending colon (a rare site) causing sub-acute intestinal obstruction. We also discuss its surgical management, differential diagnosis and review of current literature. Only a handful of cases have been reported and to the best of our knowledge none of these were from UK.