Trilateral Retinoblastoma

Abstract

INTRODUCTION Trilateral retinoblastoma (TR) is characterised by an intracranial neuroblastic tumour arising in the pineal region, associated with hereditary retinoblastomas which are usually bilateral but may also be unilateral. TR is rare, occurring in 3% of cases and is usually fatal . From August 2001 till December 2009, a total of 141 cases of retinoblastoma were seen at our institution. During this time, two children progressed to trilateral disease (1.4%).