Spontaneous Hemothorax of Tumoral Origin Complicating a Von Recklinghausen's Disease: Report of Two Cases in Cameroon and Litterature Review

Abstract

Von Recklinghausen's disease also known as neurofibromatosis type 1 (NF1), is one of the most common genetic diseases. It is responsible of the development of neurofibromas from nerve sheaths and very typical skin lesions. Chest damage according to the literature is rare. Spontaneous hemothorax is a subcategory of hemothorax that involves the accumulation of blood in the pleural space in the absence of trauma or other causes. This clinical entity secondary to vascular involvement is rarely described in the literature.