Catecholamine Induced Polymorphic Ventricular Tachycardia

Abstract

Aim: To describe a rare case of catecholamine induced polymorphic ventricular tachycardia. Presentation of Case: Intermittent attacks of Ventricular fibrillation and syncope. Summary: Catecholaminergic polymorphic ventricular tachycardia (CPVT) is a familial cardiac arrhythmia that is associated with ryanodine receptor gene (RYR2) or calsequestrin 2 (CASQ2) gene mutation. It is a rare condition that occurs in patients with structurally normal heart and leads to exercise/emotion triggered syncope and cause fatal arrhythmias. We present the case of a 21- year old female patient who was diagnosed with this condition at the age of 10 years and continues to live a healthy life. Conclusion: Patients with CPSVT require life-long beta-blockers and might need an implanted defibrator.