Point-of-care ultrasound in the assessment and monitoring of IgG4-related disease: A case report of atypical ureteral involvement

Abstract

Introduction

IgG4-related disease exhibits multi-organ involvement with predominant glandular affection. We present a case in which ultrasound proved useful for both diagnosis and follow-up. Ureteral involvement was documented as a rare manifestation.

Case summary

A 44-year-old female with increased salivary and tear glands. Ultrasound showed parenchymal heterogeneity, Zhou score of 32 points, and biopsy with positive Okazaki criteria. Treatment was started with subsequent urinary involvement and Rituximab requirement with clinical improvement and ultrasound variables in follow-up.

Conclusions

Ultrasound is a useful tool in the diagnosis and follow-up of IgG4-associated disease.