Emily C Scheffel, Lauryn A Ridley, Gabriel A Ramos, Jack Guiry, Beatriz Da Cruz Alves, Adanna C Akujuo
{"title":"Successful, Concurrent Cesarean Section and Type A Aortic Dissection Repair in a Patient With Marfan Syndrome and Sickle Cell Trait.","authors":"Emily C Scheffel, Lauryn A Ridley, Gabriel A Ramos, Jack Guiry, Beatriz Da Cruz Alves, Adanna C Akujuo","doi":"10.1155/cris/6391145","DOIUrl":null,"url":null,"abstract":"<p><p>We present a 23-year-old at 35 weeks' gestation with Marfan syndrome (MFS) and sickle cell trait (SCT) with acute Type A aortic dissection (TAAD) requiring concurrent cesarean delivery and aortic repair. Delivery, hemi-arch aortic replacement, and coronary reconstruction were successfully performed. Despite intraoperative complexity and postoperative complications, the patient was managed with fewer ischemic complications compared to previous cases of coincident SCT and aortic repair. This case demonstrates critical principles for managing cardiothoracic emergencies in pregnancy with high-risk conditions. It emphasizes multidisciplinary care and cardiopulmonary bypass (CPB) techniques for optimization of SCT and maternal-fetal outcomes in aortopathies.</p>","PeriodicalId":9600,"journal":{"name":"Case Reports in Surgery","volume":"2026 ","pages":"6391145"},"PeriodicalIF":0.6000,"publicationDate":"2026-06-18","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC13277770/pdf/","citationCount":"0","resultStr":null,"platform":"Semanticscholar","paperid":null,"PeriodicalName":"Case Reports in Surgery","FirstCategoryId":"1085","ListUrlMain":"https://doi.org/10.1155/cris/6391145","RegionNum":0,"RegionCategory":null,"ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"2026/1/1 0:00:00","PubModel":"eCollection","JCR":"Q4","JCRName":"SURGERY","Score":null,"Total":0}
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Abstract
We present a 23-year-old at 35 weeks' gestation with Marfan syndrome (MFS) and sickle cell trait (SCT) with acute Type A aortic dissection (TAAD) requiring concurrent cesarean delivery and aortic repair. Delivery, hemi-arch aortic replacement, and coronary reconstruction were successfully performed. Despite intraoperative complexity and postoperative complications, the patient was managed with fewer ischemic complications compared to previous cases of coincident SCT and aortic repair. This case demonstrates critical principles for managing cardiothoracic emergencies in pregnancy with high-risk conditions. It emphasizes multidisciplinary care and cardiopulmonary bypass (CPB) techniques for optimization of SCT and maternal-fetal outcomes in aortopathies.
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