Treatment of scleromyxedema Arndt-Gottron with a novel intravenous immunoglobulin preparation.

Abstract

Dear Editor, Scleromyxedema is known as a rare, severe mucinosis with characteristic waxy skin papules along with sclerodermiform induration of the skin and rare systemic manifestations. Monoclonal gammopathy of undetermined significance (MGUS; mostly monoclonal immunoglobulin G [IgG] type lambda) can be detected in up to 90% of patients. [...].