Multicystic Adenomatoid Pancreatic Hamartoma in a Child: Case Report.

Abstract

Multicystic adenomatoid pancreatic hamartoma (MAPH) is a rare lesion of the pancreas, particularly in the pediatric age group with only a few cases reported in the literature. We report an unusual cystic lesion diagnosed MAPH in a 26-month-old boy who presented with abdominal swelling on the right side for a period of 1 week, accompanied by icterus and itching. Magnetic resonance imaging (MRI) revealed a giant multicystic intra-abdominal mass with pressure-induced cholestasis. The large retroperitoneal lesion was completely resected. Histologically, the lesion consisted of multilocular micro- and macrocysts lined by flat, cuboidal, and columnar epithelium without atypia. The cyst walls contained notably well-formed pancreatic acini, and partially dilated ducts, and inflammatory cells, hemorrhage, edema, fibrosis with reactive fibroblasts.