Dural Sinus Malformation Involving a Persistent Transtentorial Sinus: A Rare Variant.

Abstract

This case report details a patient born with dural sinus malformation of the transtentorial sinus complicated by thrombosis, which caused compression of the fourth ventricle, venous infarction of the adjacent cerebellum, and disseminated intravascular coagulation. The enlarged, malformed pouch involved a transtentorial venous sinus, a sinus located in the tentorium cerebelli along the inner surface of the occipital bone that usually regresses before birth. The diagnosis was missed because of the rare presentation of a rare disease. In this case review, a multidisciplinary approach resulted in life-altering outcomes, with the patient meeting developmental milestones and exceeding expectations.