A Rare Cardiac Malformation: Isolated Double-Orifice Mitral Valve

Abstract

The double-orifice mitral valve (DOMV) is a rare congenital valve malformation characterized by a mitral valve with a single fibrous annulus, resulting in two orifices. Due to a lack of understanding and awareness of its echocardiographic or coronary computed tomographic angiography (CCTA) characteristics, there is a risk of misdiagnosis. We report a case of a 64-year-old woman who was found to have an isolated double orifice mitral valve malformation on transthoracic echocardiography and CCTA. Echocardiography is the first-line tool for diagnosing DOMV. CCTA is critical in the complementary diagnosis of DOMV combined with other coronary artery anomalies and extracardiac structure abnormalities.