[Research status of diagnosis, treatment and prognosis of primary Sjögren's syndrome-associated interstitial lung disease].

Abstract

Interstitial lung disease (ILD) is a group of heterogeneous non-tumor and non-infectious lung diseases with basic lesions of alveolar unit inflammation and interstitial fibrosis. There are hundreds of kinds of ILD. The study of ILD subtypes in China found that the most common disease was idiopathic pulmonary fibrosis (IPF, 26.5%), followed by CTD-ILD (24.1%). Among CTD-ILD, primary Sjögren's syndrome-associated interstitial lung disease (pSS-ILD) accounted for the largest proportion. Compared with other CTD-ILD, pSS-ILD has insidious onset and is easy to be misdiagnosed and misdiagnosed. Therefore, more extensive and in-depth studies on pSS-ILD are needed. This article reviews the research status of this disease at home and abroad, hoping to assist clinicians in diagnosing and treating this disease.