Primary Cardiac Sarcoma: A Rare Case With Superior Vena Cava Syndrome.

Abstract

Background/aim: Primary cardiac tumors, particularly sarcomas, are exceptionally rare, with limited literature available on their diagnosis and management. Patients are typically asymptomatic in the early stages of the disease, and present later with non-specific and varied symptoms.

Case report: This case describes a 59-year-old patient who presented with a cardiac mass and exhibited signs of superior vena cava syndrome, including odynophagia, dysphagia, hoarseness, and constitutional symptoms. Subsequent investigations revealed a primary malignant spindle cell sarcoma originating from the pericardium.

Conclusion: Despite treatment with chemotherapy, radiotherapy, and surgical tumor resection, the prognosis of primary cardiac spindle cell sarcoma remains poor.