Juvenile xanthogranuloma of the tongue: A case report

Abstract

Juvenile xanthogranuloma (JXG) is a rare non-Langerhans cell histiocytosis that typically presents as a self-limiting dermatological condition in young children, and oral mucosal involvement is exceedingly rare. We report the case of a 2-year-old boy, in whom a pink exophytic nodule gradually enlarged for 3 months and subsequently changed to an orange submucosal mass in approximately 1 month. Excisional biopsy was performed to obtain a definitive diagnosis. Histopathological examination revealed diffuse proliferation of foamy histiocytes and Touton giant cells within the lesion. Based on these results, the patient was diagnosed with JXG. Herein, we present an uncommon case of oral JXG to increase awareness about this lesion. The patient is currently healthy, and no recurrence has been observed 2 years after surgical excision.