Experience with etilefrine in refractory non-traumatic chylothorax: a case report.

IF 0.9 4区医学 Q4 CARDIAC & CARDIOVASCULAR SYSTEMS

Cardiology in the Young Pub Date : 2025-06-25 DOI:10.1017/S104795112510067X

Ryo Sakai, Kazuhiro Shiraga, Ryo Inuzuka

引用次数: 0

Abstract

Noonan syndrome is associated with lymphatic system structural abnormalities and may present with potentially fatal refractory chylothorax. We report a 2-year-old boy with Noonan syndrome with non-traumatic chylothorax who was refractory to dietary therapy with medium-chain triglyceride milk, octreotide, prednisolone, lymphatic embolisation, and lymphatico-venous anastomosis but improved with etilefrine administration. Etilefrine may be a treatment option for paediatric chylothorax, regardless of the aetiology.

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依替林治疗难治性非外伤性乳糜胸1例。

努南综合征与淋巴系统结构异常有关，并可能出现潜在致命的难愈乳糜胸。我们报告了一名2岁的Noonan综合征男孩，他患有非创伤性乳糜胸，他对中链甘油三酯牛奶、奥曲肽、强的松龙、淋巴栓塞和淋巴静脉吻合的饮食治疗难治性，但在给予依替林后得到改善。依替替林可能是治疗小儿乳糜胸的一种选择，无论病因如何。

本文章由计算机程序翻译，如有差异，请以英文原文为准。

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来源期刊

Cardiology in the Young 医学-小儿科

CiteScore

1.70

自引率

10.00%

发文量

715

审稿时长

4-8 weeks

期刊介绍： Cardiology in the Young is devoted to cardiovascular issues affecting the young, and the older patient suffering the sequels of congenital heart disease, or other cardiac diseases acquired in childhood. The journal serves the interests of all professionals concerned with these topics. By design, the journal is international and multidisciplinary in its approach, and members of the editorial board take an active role in the its mission, helping to make it the essential journal in paediatric cardiology. All aspects of paediatric cardiology are covered within the journal. The content includes original articles, brief reports, editorials, reviews, and papers devoted to continuing professional development.