Localised Chronic Fibrosing Vasculitis in a 6 Year Old Boy Clinically Mimicking Dermatofibrosarcoma Protuberans

Michela Brena, Italo Francesco Aromolo, Nicola Adriano Monzani, Stefano Cambiaghi, Giorgio Alberto Croci, Chiara Benaglia, Riccardo Cavalli
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Abstract

This case outlines the stepwise evaluation of a growing plaque on the back of a 6-year-old boy mimicking dermatofibrosarcoma protuberans. Further investigations, including echography and two biopsies, led to the unexpected diagnosis of Localised Chronic Fibrosing Vasculitis, highlighting the importance of considering rare entities in challenging cases.

6岁男孩局部慢性纤维化血管炎临床模拟皮肤纤维肉瘤隆突
本病例概述了对一名6岁男孩背部模仿皮肤纤维肉瘤隆突的生长斑块的逐步评估。进一步的调查,包括超声检查和两次活检,导致了局部慢性纤维化血管炎的意外诊断,强调了在具有挑战性的病例中考虑罕见实体的重要性。
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