Laura C Jorgenson, Sherry S Wang, Travis E Grotz, Rondell P Graham, Patrick J Navin, Christopher Favazza, Sudhakar K Venkatesh, Jeff L Fidler, Joel G Fletcher, Eric C Ehman, Shannon P Sheedy
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引用次数: 0
Abstract
Pseudomyxoma peritonei involves the gradual accumulation of gelatinous peritoneal metastases, typically resulting from the rupture of a mucinous appendiceal neoplasm. Standard treatment often includes cytoreductive surgery and hyperthermic intraperitoneal chemotherapy. However, recurrence is common despite optimal cytoreduction, prompting ongoing investigation into novel therapies. This comprehensive review aims to enhance radiologists' understanding of mucinous appendiceal neoplasms and pseudomyxoma peritonei by focusing on nomenclature, pathophysiology, optimal imaging strategies, and the typical imaging appearance of mucinous appendiceal neoplasm and associated peritoneal disease. It also highlights problematic areas of disease that may affect the ability to achieve complete cytoreduction or influence surgical decision making and includes a surgeon's perspective on treating this complex condition.
期刊介绍:
Launched by the Radiological Society of North America (RSNA) in 1981, RadioGraphics is one of the premier education journals in diagnostic radiology. Each bimonthly issue features 15–20 practice-focused articles spanning the full spectrum of radiologic subspecialties and addressing topics such as diagnostic imaging techniques, imaging features of a disease or group of diseases, radiologic-pathologic correlation, practice policy and quality initiatives, imaging physics, informatics, and lifelong learning.
A special issue, a monograph focused on a single subspecialty or on a crossover topic of interest to multiple subspecialties, is published each October.
Each issue offers more than a dozen opportunities to earn continuing medical education credits that qualify for AMA PRA Category 1 CreditTM and all online activities can be applied toward the ABR MOC Self-Assessment Requirement.