Joint position statement of the diagnosis and management of light chain amyloidosis and light chain cardiac amyloidosis by the Taiwan Society of Cardiology (TSOC) and the Hematology Society of Taiwan (HST).

IF 2.6 3区 医学 Q1 MEDICINE, GENERAL & INTERNAL
Yen-Wen Wu, Chao-Hung Wei, Yen-Hung Lin, Shang-Yi Huang, Yen-Wen Liu, Tran-Der Tan, Wen-Chung Yu, Chia-Jen Liu, Chung-Lieh Hung, Po-Shen Ko, Ning-I Yang, Shih-Feng Cho, Chun-Yao Huang, Chun-Kai Liao, Chieh-Lin Jerry Teng, Tsai-Yun Chen, Wen-Jone Chen, Bor-Sheng Ko
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引用次数: 0

Abstract

Light chain (AL) amyloidosis, defined by the organ deposition of misfolded and aggregated amyloid light chain, is the most common subtype of systematic amyloidosis with an incidence rate of around 1 case per 100,000 person-years in Taiwan. Due to its rarity, and heterogeneous initial presentation depending on the affected organs, diagnosis and management of AL amyloidosis are challenging. To increase the awareness of AL amyloidosis across clinical specialties and provide evidence-based recommendations, the Taiwan Society of Cardiology (TSOC) and Hematology Society of Taiwan (HST) have jointly developed a position statement. The joint statement provides diagnosis and management recommendations for systematic AL amyloidosis and AL cardiac amyloidosis under Taiwan's medical context.

台湾心脏病学会(TSOC)与台湾血液学学会(HST)对轻链淀粉样变性与心脏轻链淀粉样变性诊断与治疗的联合立场声明
轻链(AL)淀粉样变性是指错误折叠和聚集的淀粉样蛋白轻链的器官沉积,是系统性淀粉样变性最常见的亚型,台湾发病率约为每10万人年1例。由于AL淀粉样变的罕见性和不同受累器官的异质初始表现,其诊断和治疗具有挑战性。为了提高临床各专科对AL淀粉样变的认识,并提供循证建议,台湾心脏病学会(TSOC)和台湾血液学学会(HST)联合制定了一份立场声明。本联合声明提供台湾医学背景下系统性AL淀粉样变性及AL心脏淀粉样变性的诊断及治疗建议。
本文章由计算机程序翻译,如有差异,请以英文原文为准。
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来源期刊
CiteScore
6.50
自引率
6.20%
发文量
381
审稿时长
57 days
期刊介绍: Journal of the Formosan Medical Association (JFMA), published continuously since 1902, is an open access international general medical journal of the Formosan Medical Association based in Taipei, Taiwan. It is indexed in Current Contents/ Clinical Medicine, Medline, ciSearch, CAB Abstracts, Embase, SIIC Data Bases, Research Alert, BIOSIS, Biological Abstracts, Scopus and ScienceDirect. As a general medical journal, research related to clinical practice and research in all fields of medicine and related disciplines are considered for publication. Article types considered include perspectives, reviews, original papers, case reports, brief communications, correspondence and letters to the editor.
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