Symptomatic Chiari I malformation in childhood: a report of 7 cases.

R C Dauser, M A DiPietro, J L Venes
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引用次数: 62

Abstract

The Chiari I malformation, once thought to be a disorder of clinical importance only in the teen years and beyond, is now recognized as being significant in the pediatric population as well. We have reviewed 7 cases of Chiari I malformation in children less than 12 years of age. Hydrosyringomyelia was often, but not invariably, an accompanying feature, and this in turn was associated with scoliosis and motor weakness. All patients had posterior fossa and cervical decompression with dural grafting procedures, as well as various types of syringosubarachnoid shunts placed. Intraoperative ultrasound was found to be a valuable surgical adjunct. Symptoms and signs were improved or stabilized in all patients. We feel that this disorder is now more commonly reported in young children because of the increased availability of noninvasive neuroimaging techniques, especially magnetic resonance imaging. Questions are raised as to the actual incidence of undiscovered cases of this disorder in children with commonly seen conditions such as scoliosis.

儿童症状性I型恰氏体畸形7例报告
Chiari I型畸形,曾经被认为是一种仅在青少年及以后才具有临床重要性的疾病,现在被认为在儿科人群中也很重要。我们回顾了7例12岁以下儿童的基亚里氏1型畸形。脊髓空洞积水通常(但并非总是)是伴随症状,而这又与脊柱侧凸和运动无力有关。所有患者均行后颅窝和颈椎减压及硬脑膜移植手术,并放置各种类型的注射器-蛛网膜下腔分流器。术中超声是一种有价值的手术辅助手段。所有患者的症状和体征均得到改善或稳定。我们认为,由于无创神经成像技术,尤其是磁共振成像技术的发展,这种疾病在幼儿中越来越普遍。问题是提出的实际发病率未发现的情况下,这种疾病的儿童常见病,如脊柱侧凸。
本文章由计算机程序翻译,如有差异,请以英文原文为准。
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