Nasal epithelioid hemangioendothelioma - A rare case report and review of literature

Abstract

Aim

To understand the complexities in diagnosing and managing a rare case of Nasal epithelioid hemangioendothelioma, which can be clinically misdiagnosed as benign inflammatory conditions.

Background

Epithelioid hemangioendothelioma (EHE) is a rare locally invasive vascular tumor and it is characterized by proliferation of endothelial cells with epithelioid morphology. It is slow growing tumor with borderline malignant potential and has high chances of recurrence. Mostly seen in soft tissues of extremities, lungs and very rarely seen in head and neck. There are very few cases reported of EHE in nasal cavity.

Case Description

The present case report describes an unusual case of EHE of nasal cavity in a 37 year old male with 2 months history of nasal mass, obstruction and intermittent epistaxis. Patient underwent wide local excision of tumor and histopathology confirmed the diagnosis.

Conclusion

Usually wide local excision is the treatment of choice. Routinely regular follow up is advised. In cases of multiple recurrences and incompletely excised tumors radiation therapy is considered.

Clinical Significance

It is an indolent tumor which has potential for recurrence that is known to appear during adult life and unlikely to metastasize.