Cor triatrium dexter as a rare cause of central cyanosis: A case report

IF 0.6 Q4 PEDIATRICS

PROGRESS IN PEDIATRIC CARDIOLOGY Pub Date : 2025-03-19 DOI:10.1016/j.ppedcard.2025.101826

Hend A. Khalil , Rami A. Sabri , Alaa Abdorahman , Mohamed-Magdy Abuelkheir , Hany M. Abo-Haded

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引用次数: 0

Abstract

Cor triatrium dexter (CTD) is considered a rare congenital heart disease and accounts for 0.1 % of cardiac malformations. This condition occurred due to failure of regression of the right venous valve at the opening of the sinoatrial orifice in the right atrium, dividing the right atrium into 2 parts and forming a tri-atrial heart.

Case presentation: A 7-year-old child presented with fatigue and exertional dyspnea. Examination revealed oxygen saturation of 85 % and an ejection systolic murmur over the pulmonary area. Echocardiography showed moderate valvular pulmonary stenosis and a suspected membrane in the right atrium, while transesophageal echocardiography revealed a high secundum atrial septal defect (ASD) with bidirectional flow and a non-obstructive membrane in the right atrium, CTD. The patient underwent successful surgical closure of the ASD and resection of the CTD, resulting in improved oxygen saturation (98 %) and significant clinical improvement.

Conclusion, Cor triatriatum dexter is a rare congenital cardiac anomaly that can be missed on transthoracic echocardiography despite being a potential cause of central cyanosis.

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右心房三室心是一种罕见的中枢性紫绀的病因：1例报告

心房右三房（CTD）是一种罕见的先天性心脏病，占心脏畸形的0.1%。这种情况的发生是由于右心房窦房孔开口处的右静脉瓣膜退行失败，将右心房分成两部分，形成三房心。病例介绍：一名7岁儿童表现为疲劳和用力性呼吸困难。检查显示血氧饱和度85%，肺区有射血性收缩期杂音。超声心动图示中度瓣膜性肺动脉狭窄，右心房疑有膜，经食管超声心动图示高窦性房间隔缺损（ASD）伴双向血流，右心房非阻塞性膜（CTD）。患者成功完成了ASD的手术闭合和CTD的切除，改善了血氧饱和度（98%）和显著的临床改善。结论：右三心房是一种罕见的先天性心脏异常，尽管它可能是中枢性紫绀的潜在原因，但在经胸超声心动图上却可能被遗漏。

本文章由计算机程序翻译，如有差异，请以英文原文为准。

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来源期刊

PROGRESS IN PEDIATRIC CARDIOLOGY PEDIATRICS-

CiteScore

0.90

自引率

11.10%

发文量

审稿时长

75 days

期刊介绍： Progress in Pediatric Cardiology is an international journal of review presenting information and experienced opinion of importance in the understanding and management of cardiovascular diseases in children. Each issue is prepared by one or more Guest Editors and reviews a single subject, allowing for comprehensive presentations of complex, multifaceted or rapidly changing topics of clinical and investigative interest.