Cor triatrium dexter as a rare cause of central cyanosis: A case report

IF 0.6 Q4 PEDIATRICS

PROGRESS IN PEDIATRIC CARDIOLOGY Pub Date : 2025-03-19 DOI:10.1016/j.ppedcard.2025.101826

Hend A. Khalil , Rami A. Sabri , Alaa Abdorahman , Mohamed-Magdy Abuelkheir , Hany M. Abo-Haded

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Abstract

Cor triatrium dexter (CTD) is considered a rare congenital heart disease and accounts for 0.1 % of cardiac malformations. This condition occurred due to failure of regression of the right venous valve at the opening of the sinoatrial orifice in the right atrium, dividing the right atrium into 2 parts and forming a tri-atrial heart.

Case presentation: A 7-year-old child presented with fatigue and exertional dyspnea. Examination revealed oxygen saturation of 85 % and an ejection systolic murmur over the pulmonary area. Echocardiography showed moderate valvular pulmonary stenosis and a suspected membrane in the right atrium, while transesophageal echocardiography revealed a high secundum atrial septal defect (ASD) with bidirectional flow and a non-obstructive membrane in the right atrium, CTD. The patient underwent successful surgical closure of the ASD and resection of the CTD, resulting in improved oxygen saturation (98 %) and significant clinical improvement.

Conclusion, Cor triatriatum dexter is a rare congenital cardiac anomaly that can be missed on transthoracic echocardiography despite being a potential cause of central cyanosis.

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来源期刊

PROGRESS IN PEDIATRIC CARDIOLOGY PEDIATRICS-

CiteScore

0.90

自引率

11.10%

发文量

审稿时长

75 days

期刊介绍： Progress in Pediatric Cardiology is an international journal of review presenting information and experienced opinion of importance in the understanding and management of cardiovascular diseases in children. Each issue is prepared by one or more Guest Editors and reviews a single subject, allowing for comprehensive presentations of complex, multifaceted or rapidly changing topics of clinical and investigative interest.