Omphalocele and patent omphalomesenteric duct: A case report

IF 0.2 Q4 PEDIATRICS
Wassie Almaw Yigzaw, Abebe Tsegaye Danole, Abay Gosaye Wondimu
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Abstract

Introduction

The omphalomesenteric duct (OMD) is an embryonic structure that connects the yolk sac to the midgut. Under normal circumstances, it closes and self absorbes before birth. When the OMD does not obliterate, it remains patent after birth. Patent OMD are hardly ever associated with other congenital anomalies.

Case presentation

A 1-day-old term male neonate was referred to our hospital with a postnatal diagnosis of omphalocele minor. The omphalocele had not been seen on any of the prenatal ultrasounds. He was born by vaginal delivery with a weight of 2700 g. In addition to the omphalocele, the physical exam revealed a mucosal opening on the membrane of the omphalocele. A patent OMD was suspected, since meconium was draining through the mucosal opening. Abdominopelvic ultrasound showed bowel loops within the omphalocele sac. All other intra-abdominal organs appeared normal. Echocardiography revealed tricuspid atresia and a large ventricular septal defect. On the second day of life the patient was taken to the operating room for an exploratory laparotomy. The abdomen was accessed through an incision on the junction between the skin and the membrane of the omphalocele. The bowel was detached bluntly from the inner surface of the omphalocele membrane. While the bowel was exposed, a Meckel's diverticulum was found close to the ileo-cecal valve. The tip of the Meckel's diverticulum was open and fused wo the membrane of the omphalocele. We resected the segment of the small bowel that contained the Meckel's diverticulum and did an end-to-end anastomosis. After that, the omphalocele defect was closed. The patient died on the second postoperative day from his congenital heart disease.

Conclusion

Patent OMD should be suspected in patients with omphalocele who have a mucosal opening on the omphalocele membrane that drains meconium.
脐膨出伴脐肠系管未闭1例
脐肠管(OMD)是连接卵黄囊和中肠的胚胎结构。在正常情况下,它会在出生前关闭并自我吸收。如果OMD没有消失,它在出生后仍然是专利。专利OMD几乎从未与其他先天性异常相关联。病例介绍:一名出生1天的足月男婴因产后诊断为轻度脐膨出而转诊至我院。产前超声检查没有发现脐膨出。他是顺产出生的,体重2700克。除了脐膨出外,体检还发现脐膨出膜上有粘膜开口。由于胎便从粘膜开口排出,因此怀疑是先天性OMD。腹部盆腔超声显示脐膨出囊内有肠袢。其他腹内器官均正常。超声心动图显示三尖瓣闭锁和大室间隔缺损。在生命的第二天,患者被带到手术室进行探查性剖腹手术。通过皮肤和脐膨出膜交界处的切口进入腹部。肠与脐膨出膜的内表面直接分离。当肠暴露时,在回盲肠瓣附近发现了梅克尔憩室。梅克尔憩室尖端开放,与脐膨出膜融合。我们切除了包含梅克尔憩室的一小段小肠并做了端到端吻合。之后,闭合脐膨出缺损。患者在术后第二天死于先天性心脏病。结论在脐膨出膜上有排泄胎便的粘膜开口的患者应怀疑OMD未闭。
本文章由计算机程序翻译,如有差异,请以英文原文为准。
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来源期刊
CiteScore
0.60
自引率
25.00%
发文量
348
审稿时长
15 days
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