Right lung agenesis with multi-drug-resistant Cepacia syndrome: A case report.

IF 1.1 Q4 PRIMARY HEALTH CARE
Mohit Kondisetti, Priyavardhan Mishra, Anant Patil, Nikhil Sarangdhar, Sankeerth Chanamolu
{"title":"Right lung agenesis with multi-drug-resistant Cepacia syndrome: A case report.","authors":"Mohit Kondisetti, Priyavardhan Mishra, Anant Patil, Nikhil Sarangdhar, Sankeerth Chanamolu","doi":"10.4103/jfmpc.jfmpc_1424_24","DOIUrl":null,"url":null,"abstract":"<p><p>Lung agenesis (LA) is a rare congenital anomaly that refers to an absence of lung tissue and bronchi. <i>Burkholderia cepacia</i> complex (BCC) causes a fatal acute necrotising pneumonia called Cepacia syndrome. The unique concomitant association of both these rare diseases has not been highlighted in the literature to the best of our knowledge. Here, we present a case of association of right-sided lung agenesis along with Cepacia syndrome. In our case, the <i>Burkholderia cepacia</i> complex was found to be a multi-drug-resistant organism. Debilitating deterioration in the oxygen saturation was observed and initiation of treatment after culture sensitivity report yielded in remission of the disease. However, due to underlying congenital agenesis, therapeutic intervention with steroids and bronchodilators led to stabilising the patient by developing oxygenation. Underlying pulmonary congenital defects predispose individuals to infections. The implementation of antimicrobial therapy must be aided with culture and sensitivity reports for better outcomes.</p>","PeriodicalId":15856,"journal":{"name":"Journal of Family Medicine and Primary Care","volume":"14 2","pages":"804-806"},"PeriodicalIF":1.1000,"publicationDate":"2025-02-01","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC11922344/pdf/","citationCount":"0","resultStr":null,"platform":"Semanticscholar","paperid":null,"PeriodicalName":"Journal of Family Medicine and Primary Care","FirstCategoryId":"1085","ListUrlMain":"https://doi.org/10.4103/jfmpc.jfmpc_1424_24","RegionNum":0,"RegionCategory":null,"ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"2025/2/21 0:00:00","PubModel":"Epub","JCR":"Q4","JCRName":"PRIMARY HEALTH CARE","Score":null,"Total":0}
引用次数: 0

Abstract

Lung agenesis (LA) is a rare congenital anomaly that refers to an absence of lung tissue and bronchi. Burkholderia cepacia complex (BCC) causes a fatal acute necrotising pneumonia called Cepacia syndrome. The unique concomitant association of both these rare diseases has not been highlighted in the literature to the best of our knowledge. Here, we present a case of association of right-sided lung agenesis along with Cepacia syndrome. In our case, the Burkholderia cepacia complex was found to be a multi-drug-resistant organism. Debilitating deterioration in the oxygen saturation was observed and initiation of treatment after culture sensitivity report yielded in remission of the disease. However, due to underlying congenital agenesis, therapeutic intervention with steroids and bronchodilators led to stabilising the patient by developing oxygenation. Underlying pulmonary congenital defects predispose individuals to infections. The implementation of antimicrobial therapy must be aided with culture and sensitivity reports for better outcomes.

求助全文
约1分钟内获得全文 求助全文
来源期刊
自引率
7.10%
发文量
884
审稿时长
40 weeks
×
引用
GB/T 7714-2015
复制
MLA
复制
APA
复制
导出至
BibTeX EndNote RefMan NoteFirst NoteExpress
×
提示
您的信息不完整,为了账户安全,请先补充。
现在去补充
×
提示
您因"违规操作"
具体请查看互助需知
我知道了
×
提示
确定
请完成安全验证×
copy
已复制链接
快去分享给好友吧!
我知道了
右上角分享
点击右上角分享
0
联系我们:info@booksci.cn Book学术提供免费学术资源搜索服务,方便国内外学者检索中英文文献。致力于提供最便捷和优质的服务体验。 Copyright © 2023 布克学术 All rights reserved.
京ICP备2023020795号-1
ghs 京公网安备 11010802042870号
Book学术文献互助
Book学术文献互助群
群 号:481959085
Book学术官方微信