DERMATOFIBROSARCOMA PROTUBERANS: WIDE LOCAL EXCISION AS DERMATOSURGICAL APPROACH WITH FAVOURABLE FINAL OUTCOME-CASE PRESENTATION AND SHORT UPDATE ON THERAPEUTIC OPTIONS.

Q4 Medicine
Georgian medical news Pub Date : 2024-10-01
G Tchernev, V Broshtilova, S Kordeva
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引用次数: 0

Abstract

Dermatofibrosarcoma protuberans (DFSP) is a rare, low-grade cutaneous sarcoma typically found on the proximal extremities and the trunk, characterized by infiltrative growth and low risk of metastasis. High rates of local recurrence or relatively large tumor sizes can significantly complicate therapeutic management, particularly when 1) surgical intervention is not adequately performed and /or 2 access to newer medications is limited or their high cost imposes a financial burden on patients. We present the case of a 63-year-old male with a histologically confirmed dermatofibrosarcoma protuberans, measuring 6 cm in diameter, located on the right dorsal region, accompanied by several confluent multifocal nodules situated infralaterally to the primary formation. Wide surgical excision with 5 mm margins in all directions was performed, achieving clean resection margins in all directions and short term recidive-free outcome. This report also provides a brief overview of the therapeutic options available for DFSP, emphasizing the surgical approach, which remains the gold standard for treatment.

皮肤纤维肉瘤隆突:广泛的局部切除作为皮肤外科方法,具有良好的最终结果,病例介绍和治疗方案的简短更新。
隆突性皮肤纤维肉瘤(DFSP)是一种罕见的低级别皮肤肉瘤,通常发生在四肢近端和躯干,以浸润性生长和低转移风险为特征。高局部复发率或相对较大的肿瘤大小会使治疗管理变得非常复杂,特别是当1)手术干预不充分和/或2获得新药物的机会有限或其高昂的费用给患者带来经济负担时。我们报告一例63岁男性的病例,组织学证实为皮肤纤维肉瘤突起,直径6厘米,位于右背区,并伴有几个位于原发形成侧侧的融合多灶结节。在所有方向上进行5 mm边缘的广泛手术切除,实现了所有方向的清洁切除边缘和短期无复发的结果。本报告还简要概述了DFSP的治疗选择,强调手术方法仍然是治疗的金标准。
本文章由计算机程序翻译,如有差异,请以英文原文为准。
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来源期刊
Georgian medical news
Georgian medical news Medicine-Medicine (all)
CiteScore
0.60
自引率
0.00%
发文量
207
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