Segev Gabay, Moran Hausman-Kedem, Udi Sadeh Gonik, Tali Jonash-Kimchi, Shelly Shiran, Rene Chapot, Jonathan Roth, Zvi Lidar, Dror Ofir
{"title":"Pediatric metameric cervical spinal cord arteriovenous malformation managed with staged endovascular and spinal stabilization approach: a case report.","authors":"Segev Gabay, Moran Hausman-Kedem, Udi Sadeh Gonik, Tali Jonash-Kimchi, Shelly Shiran, Rene Chapot, Jonathan Roth, Zvi Lidar, Dror Ofir","doi":"10.1038/s41394-024-00691-w","DOIUrl":null,"url":null,"abstract":"<p><strong>Introduction: </strong>Spinal cord arteriovenous malformations (SCAVM) are rare congenital vascular malformations, characterized by two or more AVMs affecting any of the spinal segments. SCAVM has complex pathophysiology and may be associated with acute, or progressively neurological deficits.</p><p><strong>Case presentation: </strong>A 12-year old girl, presented with progressive neurologic deficits secondary to compressive cervical myelopathy due to a cervical metameric SCAVM. She was successfully treated with a staged surgical-endovascular approach and regained normal neurological function with radiological stability.</p><p><strong>Discussion: </strong>SCAVM is a rare disease with complex management, and in many cases, the treatment is focused on palliative care. With multimodality management, of a combined surgical-endovascular approach, the patient achieved neurological, functional, and structural stability over the follow-up period.</p>","PeriodicalId":22079,"journal":{"name":"Spinal Cord Series and Cases","volume":"10 1","pages":"80"},"PeriodicalIF":0.7000,"publicationDate":"2024-12-11","publicationTypes":"Journal Article","fieldsOfStudy":null,"isOpenAccess":false,"openAccessPdf":"https://www.ncbi.nlm.nih.gov/pmc/articles/PMC11634885/pdf/","citationCount":"0","resultStr":null,"platform":"Semanticscholar","paperid":null,"PeriodicalName":"Spinal Cord Series and Cases","FirstCategoryId":"1085","ListUrlMain":"https://doi.org/10.1038/s41394-024-00691-w","RegionNum":0,"RegionCategory":null,"ArticlePicture":[],"TitleCN":null,"AbstractTextCN":null,"PMCID":null,"EPubDate":"","PubModel":"","JCR":"Q4","JCRName":"CLINICAL NEUROLOGY","Score":null,"Total":0}
引用次数: 0
Abstract
Introduction: Spinal cord arteriovenous malformations (SCAVM) are rare congenital vascular malformations, characterized by two or more AVMs affecting any of the spinal segments. SCAVM has complex pathophysiology and may be associated with acute, or progressively neurological deficits.
Case presentation: A 12-year old girl, presented with progressive neurologic deficits secondary to compressive cervical myelopathy due to a cervical metameric SCAVM. She was successfully treated with a staged surgical-endovascular approach and regained normal neurological function with radiological stability.
Discussion: SCAVM is a rare disease with complex management, and in many cases, the treatment is focused on palliative care. With multimodality management, of a combined surgical-endovascular approach, the patient achieved neurological, functional, and structural stability over the follow-up period.