[An unusual case of bicuspid aortic valve in adult age].

IF 0.7 Q4 CARDIAC & CARDIOVASCULAR SYSTEMS
Luca Bergamasco, Stefano Maffè, Paola Paffoni, Emanuela Facchini, Nicolò Franchetti Pardo, Eleonora Prenna, Pasquale Fabroccini, Pierfranco Dellavesa
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引用次数: 0

Abstract

A 38-year-old man was evaluated for heart palpitations and chest pain diagnosed with atrial fibrillation, left ventricular ejection fraction 30%, and moderate aortic insufficiency. On echocardiographic control, evidence of aortic bicuspid valve and aortic coarctation on the isthmus with dilated epiaortic vessels. Computed tomography angiography confirmed the presence of aortic coarctation of the descending portion of the arch with supply of the thoracic aorta by collateral vessels originating from the brachiocephalic vessels. The patient underwent two surgical procedures, the first to correct the aortic coarctation in left posterior lateral thoracotomy, the second to repair the aortic valve with valvuloplasty. At the remote re-evaluation, the patient presented in good general and compensatory conditions, in stable sinus rhythm and with a left ventricular systolic function at the lower limits. Aortic coarctation accounts for about 8% of all congenital heart diseases, and bicuspid aortic valve is associated with congenital heart disease in 85% of cases. The peculiarity of the case is the type of vessel malformation considered as an aortic "atresia". The late presentation in a patient previously in substantial well-being is also unusual. Finally, the near normalization of cardiac function after surgery is important.

[一例罕见的成人主动脉瓣双尖瓣病例]。
一名 38 岁男子因心悸和胸痛接受评估,被诊断为心房颤动、左室射血分数 30%、中度主动脉瓣关闭不全。经超声心动图检查,发现主动脉双尖瓣和主动脉峡部的主动脉瓣闭锁,上主动脉血管扩张。计算机断层扫描血管造影证实,主动脉弓降部存在主动脉闭塞,胸主动脉由源自肱脑血管的侧支血管供应。患者接受了两次手术,第一次是在左后外侧开胸手术中矫正主动脉瓣闭锁,第二次是通过瓣膜成形术修复主动脉瓣。在远期再次评估时,患者全身状况和代偿状况良好,窦性心律稳定,左心室收缩功能处于下限。主动脉瓣狭窄约占所有先天性心脏病的 8%,而主动脉瓣双尖裂则有 85% 的病例与先天性心脏病有关。该病例的特殊之处在于其血管畸形类型被视为主动脉 "闭锁"。此外,该病例的发病时间较晚,而患者之前的状况良好,这也是不寻常的。最后,手术后心脏功能接近正常也很重要。
本文章由计算机程序翻译,如有差异,请以英文原文为准。
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来源期刊
Giornale italiano di cardiologia
Giornale italiano di cardiologia CARDIAC & CARDIOVASCULAR SYSTEMS-
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1.10
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