Pseudotumoral portal cavernoma: A rare case that challenges diagnosis

Q4 Medicine

Radiology Case Reports Pub Date : 2024-10-30 DOI:10.1016/j.radcr.2024.09.136

Fadwa Jaheddine MD, Kaoutar Imrani PhD, Hiba Zahi MD, Nabil Moatassim Billah PhD, Ittimade Nassar PhD

引用次数: 0

Abstract

Portal cavernoma cholangiopathy (PCC), also known as portal biliopathy, refers to biliary duct abnormalities caused by extrahepatic portal vein obstruction (EHPVO) and subsequent cavernous transformation of the portal vein. Pseudotumoral portal cavernoma is a specific subtype of PCC characterized by the presence of numerous thin collateral veins that mimic the sheath of the common bile duct (CBD). We present a case of a 42-year-old women with pseudotumoral portal cavernoma secondary to portal vein thrombosis, a complication of myeloproliferative disorder. This case underscores the diagnostic challenges posed by pseudotumoral portal cavernoma and emphasizes the crucial role of imaging in achieving an accurate diagnosis.

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假瘤门海绵状瘤：挑战诊断的罕见病例

门静脉海绵状瘤胆管病（PCC）又称门静脉胆管病，是指由肝外门静脉阻塞（EHPVO）和随后的门静脉海绵状变引起的胆管异常。假瘤型门静脉海绵状瘤是 PCC 的一种特殊亚型，其特点是存在许多模仿总胆管（CBD）鞘的细侧静脉。我们介绍了一例继发于门静脉血栓（骨髓增生性疾病的并发症）的 42 岁女性假瘤型门静脉海绵状瘤患者。该病例凸显了假瘤性门海绵状瘤给诊断带来的挑战，并强调了影像学在实现准确诊断中的关键作用。

本文章由计算机程序翻译，如有差异，请以英文原文为准。

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来源期刊

Radiology Case Reports Medicine-Radiology, Nuclear Medicine and Imaging

CiteScore

1.10

自引率

0.00%

发文量

1074

审稿时长

30 days

期刊介绍： The content of this journal is exclusively case reports that feature diagnostic imaging. Categories in which case reports can be placed include the musculoskeletal system, spine, central nervous system, head and neck, cardiovascular, chest, gastrointestinal, genitourinary, multisystem, pediatric, emergency, women''s imaging, oncologic, normal variants, medical devices, foreign bodies, interventional radiology, nuclear medicine, molecular imaging, ultrasonography, imaging artifacts, forensic, anthropological, and medical-legal. Articles must be well-documented and include a review of the appropriate literature.