Real-Life Experience with CFTR Modulators Shows Correction of LAD-IV Phenotype in Cystic Fibrosis.

IF 5.9 2区医学 Q1 BIOCHEMISTRY & MOLECULAR BIOLOGY

American Journal of Respiratory Cell and Molecular Biology Pub Date : 2024-10-01 DOI:10.1165/rcmb.2024-0136LE

Alessio Montresor, Beatrice D'Ulivo, Sara Preato, Alessia Farinazzo, Emily Pintani, Elena Dalla Chiara, Lorena Torroni, Giuseppe Verlato, Silvia Boscia, Laura Pisano, Giusi Mangone, Silvia Ricci, Chiara Azzari, Giovanni Taccetti, Vito Terlizzi, Marco Cipolli, Paola Melotti, Claudio Sorio, Carlo Laudanna

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使用 CFTR 调节剂的实际经验显示，囊性纤维化患者的 LAD-IV 表型得到了纠正。

本文章由计算机程序翻译，如有差异，请以英文原文为准。

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来源期刊

American Journal of Respiratory Cell and Molecular Biology 生物-呼吸系统

CiteScore

11.20

自引率

3.10%

发文量

370

审稿时长

3-8 weeks

期刊介绍： The American Journal of Respiratory Cell and Molecular Biology publishes papers that report significant and original observations in the area of pulmonary biology. The focus of the Journal includes, but is not limited to, cellular, biochemical, molecular, developmental, genetic, and immunologic studies of lung cells and molecules.