Ectopic urethral opening in herlyn-werner-wunderlich syndrome: A rare finding

Abstract

Recorded findings of Herlyn-Werner-Wunderlich Syndrome (HWWS) remain sparse due to low statistical incidence. Ours is also the first known case to present with an ectopic urethral opening, an even rarer complication. A 27-year-old nulliparous woman presented with complaints of cyclical hematuria, and burning micturition with intermittent episodes of urinary retention suprapubic and pelvic pain. After extensive radiological examination, the MRI findings concluded the presence of a uterine didelphys with 2 cervixes and vaginal duplication marked by the compression of the left hemivagina and dilation of the right hemivagina, pointing towards HWWS. The case strongly suggests that the presence of an ectopic urethral opening may be the cause of urinary incontinence and discomfort in an otherwise asymptomatic patient of HWWS.