Dehiscencia de suturas en pacientes con enfermedad del tejido conectivo: síndromes de Marfan y Weill-Marchesani

Q3 Medicine

Archivos De La Sociedad Espanola De Oftalmologia Pub Date : 2024-11-01 DOI:10.1016/j.oftal.2024.06.010

M. de las M. Valentín-Pastrana Aguilar , I. Platas Moreno , N. Muñoz Sanz , B. Sandoval Cortés , J. Herrera Pereiro , I. Jiménez-Alfaro Morote

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引用次数: 0

Abstract

Marfan and Weill-Marchesani syndromes have a mutation of the fibrillin gene (FBN1), producing alteration of connective tissue, within ophthalmology, it is important to take into consideration this type of diseases in cogenetic alterations in this system will produce modifications at the level of the ocular structures generating problems of various types, Most of the literature refers to ectopia lentis and the complications derived from it, as secondary glaucoma.

We present two patients, one with Marfan syndrome and the other with Weill-Marchesani syndrome, who developed lens dislocation, typical of their pathologies, which led them to undergo different surgeries. Both developed suture dehiscence after these surgeries, as a complication derived from their connective tissue involvement. We thus highlight the need for vigilance and extreme caution in the postoperative period of patients affected by this type of syndromes.

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结缔组织病患者缝线开裂：马凡综合征和魏尔-马切萨尼综合征。

马凡综合征和魏尔-马切萨尼综合征的纤维蛋白基因（FBN1）发生突变，导致结缔组织发生改变，在眼科领域，必须考虑到这类疾病，因为该系统的遗传改变会导致眼部结构发生改变，从而引发各种问题。我们介绍了两名患者，一名患有马凡氏综合征，另一名患有魏尔-马切萨尼综合征，他们都出现了晶状体脱位，这是他们的典型病症，导致他们接受了不同的手术。两人在手术后都出现了缝线开裂，这是结缔组织受累引起的并发症。因此，我们强调在此类综合征患者的术后阶段需要保持警惕和格外小心。

本文章由计算机程序翻译，如有差异，请以英文原文为准。

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来源期刊

Archivos De La Sociedad Espanola De Oftalmologia Medicine-Ophthalmology

CiteScore

1.20

自引率

0.00%

发文量

109

审稿时长

78 days

期刊介绍： La revista Archivos de la Sociedad Española de Oftalmología, editada mensualmente por la propia Sociedad, tiene como objetivo publicar trabajos de investigación básica y clínica como artículos originales; casos clínicos, innovaciones técnicas y correlaciones clinicopatológicas en forma de comunicaciones cortas; editoriales; revisiones; cartas al editor; comentarios de libros; información de eventos; noticias personales y anuncios comerciales, así como trabajos de temas históricos y motivos inconográficos relacionados con la Oftalmología. El título abreviado es Arch Soc Esp Oftalmol, y debe ser utilizado en bibliografías, notas a pie de página y referencias bibliográficas.