Oral and maxillofacial manifestations in young patients with Hyalin fibromatosis syndrome: A case series

Q3 Dentistry

Oral and Maxillofacial Surgery Cases Pub Date : 2024-06-20 DOI:10.1016/j.omsc.2024.100362

Iman Malakuti , Anna Persson , Anders Näsman , Gunnar Liminga , Petter Gavelin , Andreas Thor

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引用次数: 0

Abstract

Study design

Case report.

Objective

To present two cases of young children with Hyaline Fibromatosis Syndrome and their oral and maxillofacial manifestations.

Methods

The different oral and maxillofacial manifestations were clinically examined in detail. The patients were treated with surgical excisions of their gingival hyperplasias and soft tissue tumors of the head.

Results

Relief of pain from ears, scalp and intraoral was obtained, resulting in a normal eating and nutritional habits despite absence of teeth. Improved esthetics.

Conclusion

This paper underscores the importance of early diagnosis and prompt therapeutic interventions in managing Hyaline Fibromatosis Syndrome. This report contributes to the growing body of knowledge regarding this rare disorder and emphasizes the importance of a multidisciplinary approach in achieving favorable outcomes for patients afflicted with HFS.

查看原文本刊更多论文

海林纤维瘤病综合征年轻患者的口腔和颌面部表现：病例系列

研究设计病例报告。目的介绍两例患有透明纤维瘤病综合征的幼儿及其口腔和颌面部表现。方法对不同的口腔和颌面部表现进行详细的临床检查。结果患者的耳朵、头皮和口腔内疼痛得到缓解，尽管没有牙齿，但饮食和营养习惯正常。结论本文强调了早期诊断和及时治疗对治疗透明纤维瘤综合症的重要性。本报告有助于加深人们对这种罕见疾病的了解，并强调了多学科方法对 HFS 患者取得良好疗效的重要性。

本文章由计算机程序翻译，如有差异，请以英文原文为准。

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来源期刊

Oral and Maxillofacial Surgery Cases Medicine-Otorhinolaryngology

CiteScore

0.60

自引率

0.00%

发文量

审稿时长

69 days

期刊介绍： Oral and Maxillofacial Surgery Cases is a surgical journal dedicated to publishing case reports and case series only which must be original, educational, rare conditions or findings, or clinically interesting to an international audience of surgeons and clinicians. Case series can be prospective or retrospective and examine the outcomes of management or mechanisms in more than one patient. Case reports may include new or modified methodology and treatment, uncommon findings, and mechanisms. All case reports and case series will be peer reviewed for acceptance for publication in the Journal.